1 / 1 DeCS    
Descriptor English:   Hyperlipoproteinemia Type IV 
Descriptor Spanish:   Hiperlipoproteinemia Tipo IV 
Descriptor Portuguese:   Hiperlipoproteinemia Tipo IV 
Synonyms English:   Carbohydrate Inducible Hyperlipemia
Carbohydrate Inducible Hyperlipemias
Carbohydrate-Inducible Hyperlipemia
Carbohydrate-Inducible Hyperlipemias
Familial Hyperlipoproteinemia Type 4
Familial Hypertriglyceridemia
Familial Type IV Hyperlipoproteinemia
Hyper prebeta lipoproteinemia
Hyperlipemia, Carbohydrate Inducible
Hyperlipemia, Carbohydrate-Inducible
Hyperlipemias, Carbohydrate Inducible
Hyperlipemias, Carbohydrate-Inducible
Hyperlipoproteinemia, Type IV
Hyperlipoproteinemias, Type IV
Hyperprebetalipoproteinemia
Hypertriglyceridemia, Familial
Inducible Hyperlipemia, Carbohydrate
Inducible Hyperlipemias, Carbohydrate
Type IV Hyperlipoproteinemia
Type IV Hyperlipoproteinemias
Type IV, Hyperlipoproteinemia  
Tree Number:   C16.320.565.398.487
C18.452.584.500.500.644.490
C18.452.584.500.500.851.500
C18.452.648.398.487
Definition English:   A hypertriglyceridemia disorder, often with autosomal dominant inheritance. It is characterized by the persistent elevations of plasma TRIGLYCERIDES, endogenously synthesized and contained predominantly in VERY-LOW-DENSITY LIPOPROTEINS (pre-beta lipoproteins). In contrast, the plasma CHOLESTEROL and PHOSPHOLIPIDS usually remain within normal limits. 
History Note English:   80 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   7134 
Unique Identifier:   D006953 


   DISEASES [C]
      Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
         Genetic Diseases, Inborn [C16.320]
            Metabolism, Inborn Errors [C16.320.565]
               Amino Acid Metabolism, Inborn Errors [C16.320.565.100] +
               Amino Acid Transport Disorders, Inborn [C16.320.565.151] +
               Amyloidosis, Familial [C16.320.565.176] +
               Brain Diseases, Metabolic, Inborn [C16.320.565.189] +
               Carbohydrate Metabolism, Inborn Errors [C16.320.565.202] +
               Cytochrome-c Oxidase Deficiency [C16.320.565.240]
               Hyperbilirubinemia, Hereditary [C16.320.565.300] +
               Lipid Metabolism, Inborn Errors [C16.320.565.398]
                  Barth Syndrome [C16.320.565.398.224]
                  Hyperlipidemia, Familial Combined [C16.320.565.398.450]
                  Hyperlipoproteinemia Type I [C16.320.565.398.465]
                  Hyperlipoproteinemia Type II [C16.320.565.398.481]
                  Hyperlipoproteinemia Type III [C16.320.565.398.483]
                  Hyperlipoproteinemia Type IV [C16.320.565.398.487] 
                  Hyperlipoproteinemia Type V [C16.320.565.398.493]
                  Hypolipoproteinemias [C16.320.565.398.500] +
                  Lipidoses [C16.320.565.398.641] +
                  Lipodystrophy, Congenital Generalized [C16.320.565.398.745]
                  Smith-Lemli-Opitz Syndrome [C16.320.565.398.850]
                  Xanthomatosis, Cerebrotendinous [C16.320.565.398.925]
               Lysosomal Storage Diseases [C16.320.565.595] +
               Metal Metabolism, Inborn Errors [C16.320.565.618] +
               Peroxisomal Disorders [C16.320.565.663] +
               Progeria [C16.320.565.753]
               Purine-Pyrimidine Metabolism, Inborn Errors [C16.320.565.798] +
               Renal Tubular Transport, Inborn Errors [C16.320.565.893]
               Steroid Metabolism, Inborn Errors [C16.320.565.925] +


   DISEASES [C]
      Nutritional and Metabolic Diseases [C18]
         Metabolic Diseases [C18.452]
            Lipid Metabolism Disorders [C18.452.584]
               Dyslipidemias [C18.452.584.500]
                  Hyperlipidemias [C18.452.584.500.500]
                     Hypercholesterolemia [C18.452.584.500.500.396]
                     Hyperlipidemia, Familial Combined [C18.452.584.500.500.438]
                     Hyperlipoproteinemias [C18.452.584.500.500.644]
                        Hyperlipoproteinemia Type I [C18.452.584.500.500.644.237]
                        Hyperlipoproteinemia Type II [C18.452.584.500.500.644.475]
                        Hyperlipoproteinemia Type III [C18.452.584.500.500.644.485]
                        Hyperlipoproteinemia Type IV [C18.452.584.500.500.644.490] 
                        Hyperlipoproteinemia Type V [C18.452.584.500.500.644.495]
                     Hypertriglyceridemia [C18.452.584.500.500.851] +


   DISEASES [C]
      Nutritional and Metabolic Diseases [C18]
         Metabolic Diseases [C18.452]
            Lipid Metabolism Disorders [C18.452.584]
               Dyslipidemias [C18.452.584.500]
                  Hyperlipidemias [C18.452.584.500.500]
                     Hypercholesterolemia [C18.452.584.500.500.396]
                     Hyperlipidemia, Familial Combined [C18.452.584.500.500.438]
                     Hyperlipoproteinemias [C18.452.584.500.500.644] +
                     Hypertriglyceridemia [C18.452.584.500.500.851]
                        Hyperlipoproteinemia Type IV [C18.452.584.500.500.851.500] 
                        Hyperlipoproteinemia Type V [C18.452.584.500.500.851.750]
                        Hypertriglyceridemic Waist [C18.452.584.500.500.851.875]


   DISEASES [C]
      Nutritional and Metabolic Diseases [C18]
         Metabolic Diseases [C18.452]
            Metabolism, Inborn Errors [C18.452.648]
               Amino Acid Metabolism, Inborn Errors [C18.452.648.100] +
               Amino Acid Transport Disorders, Inborn [C18.452.648.151] +
               Amyloidosis, Familial [C18.452.648.176] +
               Brain Diseases, Metabolic, Inborn [C18.452.648.189] +
               Carbohydrate Metabolism, Inborn Errors [C18.452.648.202] +
               Hyperbilirubinemia, Hereditary [C18.452.648.300] +
               Lipid Metabolism, Inborn Errors [C18.452.648.398]
                  Barth Syndrome [C18.452.648.398.224]
                  Hyperlipidemia, Familial Combined [C18.452.648.398.450]
                  Hyperlipoproteinemia Type I [C18.452.648.398.465]
                  Hyperlipoproteinemia Type II [C18.452.648.398.481]
                  Hyperlipoproteinemia Type III [C18.452.648.398.483]
                  Hyperlipoproteinemia Type IV [C18.452.648.398.487] 
                  Hyperlipoproteinemia Type V [C18.452.648.398.493]
                  Hypolipoproteinemias [C18.452.648.398.500] +
                  Lipidoses [C18.452.648.398.641] +
                  Lipodystrophy, Congenital Generalized [C18.452.648.398.745]
                  Smith-Lemli-Opitz Syndrome [C18.452.648.398.850]
                  Xanthomatosis, Cerebrotendinous [C18.452.648.398.925]
               Lysosomal Storage Diseases [C18.452.648.595] +
               Metal Metabolism, Inborn Errors [C18.452.648.618] +
               Peroxisomal Disorders [C18.452.648.663] +
               Progeria [C18.452.648.753]
               Purine-Pyrimidine Metabolism, Inborn Errors [C18.452.648.798] +
               Renal Tubular Transport, Inborn Errors [C18.452.648.893]
               Steroid Metabolism, Inborn Errors [C18.452.648.925] +