Descriptors Found: 1
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Descriptor English:   Malignant Atrophic Papulosis 
Descriptor Spanish:   Papulosis Atrófica Maligna 
Descriptor Portuguese:   Papulose Atrófica Maligna 
Synonyms English:   Atrophic Papuloses, Malignant
Atrophic Papulosis, Malignant
Degos Disease
Degos Syndrome
Degos's Malignant Atrophic Papulosis
Disease, Degos
Disease, Kohlmeier-Degos
Erythrokeratoderma en cocardes
Kohlmeier-Degos Disease
Malignant Atrophic Papuloses
Papuloses, Malignant Atrophic
Papulosis, Malignant Atrophic
Syndrome, Degos  
Tree Number:   C14.907.137.520
Definition English:   Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. 
Indexing Annotation English:   malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA
History Note English:   2008 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   52617 
Unique Identifier:   D054853 

Occurrence in VHL: