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Descriptor English:   Neoplastic Syndromes, Hereditary 
Descriptor Spanish:   Síndromes Neoplásicos Hereditarios 
Descriptor Portuguese:   Síndromes Neoplásicas Hereditárias 
Synonyms English:   Cancer Syndrome, Hereditary
Cancer Syndromes, Hereditary
Hereditary Cancer Syndrome
Hereditary Cancer Syndromes
Hereditary Neoplastic Syndrome
Hereditary Neoplastic Syndromes
Neoplastic Syndrome, Hereditary
Syndrome, Hereditary Cancer
Syndrome, Hereditary Neoplastic
Syndromes, Hereditary Cancer
Syndromes, Hereditary Neoplastic  
Tree Number:   C04.700
Definition English:   The condition of a pattern of malignancies within a family, but not every individual's necessarily having the same neoplasm. Characteristically the tumor tends to occur at an earlier than average age, individuals may have more than one primary tumor, the tumors may be multicentric, usually more than 25 percent of the individuals in direct lineal descent from the proband are affected, and the cancer predisposition in these families behaves as an autosomal dominant trait with about 60 percent penetrance. 
Indexing Annotation English:   coordinate with specific hereditary organ/neoplasm term or specific hereditary histological type
History Note English:   87 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   19258 
Unique Identifier:   D009386 

Occurrence in VHL: