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Descriptor English: Incontinentia Pigmenti
Descriptor Spanish: Incontinencia Pigmentaria
Descriptor incontinencia pigmentaria
Entry term(s) síndrome de Bloch-Sulzberger
Scope note: Genodermatosis que aparece fundamentalmente en mujeres y que se caracteriza por cambios cutáneos en tres fases - vesiculobullosa, verrugosa papilomatosa, y macular melanodérmica. La hiperpigmentación es bizarra e irregular. El sesenta por ciento de los pacientes tiene anomalías en los ojos, dientes, sistema nervioso central, y apéndices cutáneos.
Descriptor Portuguese: Incontinência Pigmentar
Descriptor French: Incontinentia pigmenti
Entry term(s): Dermatose pigmentaire en éclaboussures
Mélanose dégénérative du chorion
Naevus chromatophore héréditaire
Syndrome de Bloch-Sulzberger
Tree number(s): C16.131.077.445
C16.131.831.580
C16.320.850.420
C17.800.621.497
C17.800.804.580
C17.800.827.420
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D007184
Scope note: A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Annotation: multiple skin & other abnorm; do not confuse with INCONTINENTIA PIGMENTI ACHROMIANS see PIGMENTATION DISORDERS
Allowable Qualifiers: BL sang
CF liquide cérébrospinal
CI induit chimiquement
CL classification
CO complications
DG imagerie diagnostique
DH diétothérapie
DI diagnostic
DT traitement médicamenteux
EC économie
EH ethnologie
EM embryologie
EN enzymologie
EP épidémiologie
ET étiologie
GE génétique
HI histoire
IM immunologie
ME métabolisme
MI microbiologie
MO mortalité
NU soins infirmiers
PA anatomopathologie
PC prévention et contrôle
PP physiopathologie
PS parasitologie
PX psychologie
RH rééducation et réadaptation
RT radiothérapie
SU chirurgie
TH thérapie
UR urine
VE médecine vétérinaire
VI virologie
DeCS ID: 19206
Unique ID: D007184
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1991/01/01
Date of Entry: 1986/04/03
Revision Date: 2016/07/01
Incontinentia pigmenti - Preferred
Concept UI M0011200
Preferred term Incontinentia pigmenti
Entry term(s) Dermatose pigmentaire en éclaboussures
Mélanose dégénérative du chorion
Naevus chromatophore héréditaire
Syndrome de Bloch-Sulzberger



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