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Descriptor English: Ichthyosiform Erythroderma, Congenital
Descriptor Spanish: Eritrodermia Ictiosiforme Congénita
Descriptor eritrodermia ictiosiforme congénita
Scope note: Este término se utiliza para designar algunas formas graves de ictiosis observadas en el recien naciod, que se caracteriza por escamas hiperquerotósicas. Los neonatos pueden encontrarse envueltos en una membrana coloide que puede comenzar a desprenderse en las primeras 24 horas. A lo largo de las dos semanas siguientes se produce un proceso de descamación persistente. De esta enfermedad exisiten formas bullosas (HIPERQUERATOSIS EPIDERMOLÍTICA), no bullosas, (ICTIOSIS LAMELAR), de tipo húmedo y seco.
Descriptor Portuguese: Eritrodermia Ictiosiforme Congênita
Descriptor French: Érythrodermie ichtyosiforme congénitale
Entry term(s): Érythrodermie ichtyosiforme congénitale humide
Érythrodermie ichtyosiforme congénitale sèche
Tree number(s): C16.131.831.512.400
C16.320.850.400
C16.614.492.400
C17.800.428.333.250
C17.800.804.512.400
C17.800.827.400
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D016113
Scope note: Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
Annotation: an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
Allowable Qualifiers: BL sang
CF liquide cérébrospinal
CI induit chimiquement
CL classification
CO complications
DG imagerie diagnostique
DH diétothérapie
DI diagnostic
DT traitement médicamenteux
EC économie
EH ethnologie
EM embryologie
EN enzymologie
EP épidémiologie
ET étiologie
GE génétique
HI histoire
IM immunologie
ME métabolisme
MI microbiologie
MO mortalité
NU soins infirmiers
PA anatomopathologie
PC prévention et contrôle
PP physiopathologie
PS parasitologie
PX psychologie
RH rééducation et réadaptation
RT radiothérapie
SU chirurgie
TH thérapie
UR urine
VE médecine vétérinaire
VI virologie
DeCS ID: 28985
Unique ID: D016113
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1991/01/01
Date of Entry: 1990/02/12
Revision Date: 2015/06/18
Érythrodermie ichtyosiforme congénitale - Preferred
Concept UI M0024612
Preferred term Érythrodermie ichtyosiforme congénitale
Érythrodermie ichtyosiforme congénitale humide - Narrower
Concept UI M0024614
Preferred term Érythrodermie ichtyosiforme congénitale humide
Érythrodermie ichtyosiforme congénitale sèche - Narrower
Concept UI M0024613
Preferred term Érythrodermie ichtyosiforme congénitale sèche



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