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Descriptor English: | Leukokeratosis, Hereditary Mucosal | ||||||
Descriptor Spanish: |
Leucoqueratosis Mucosa Hereditaria
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Descriptor Portuguese: | Leucoceratose da Mucosa Hereditária | ||||||
Descriptor French: | Naevus spongieux de Cannon | ||||||
Entry term(s): |
Kératose héréditaire des muqueuses Leucokératose héréditaire des muqueuses Maladie de Cannon Naevus blanc spongieux Naevus blanc spongieux de Cannon Naevus blanc spongieux des muqueuses Naevus de Cannon White Sponge Naevus |
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Tree number(s): |
C16.320.850.542 C17.800.827.595 |
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RDF Unique Identifier: | https://id.nlm.nih.gov/mesh/D053529 | ||||||
Scope note: | An autosomal dominant disorder that is manifested by thickened spongiform ORAL MUCOSA with a white opalescent tint. Other MUCOSAL TISSUE may also be involved mucosa found in the VAGINA; RECTUM, and NASAL CAVITY may be similarly involved. This form of LEUKOKERATOSIS can be caused by a mutation in the gene for KERATIN 4 and is not considered a PRENEOPLASTIC CONDITION. |
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Allowable Qualifiers: |
BL sang CF liquide cérébrospinal CI induit chimiquement CL classification CO complications DG imagerie diagnostique DH diétothérapie DI diagnostic DT traitement médicamenteux EC économie EH ethnologie EM embryologie EN enzymologie EP épidémiologie ET étiologie GE génétique HI histoire IM immunologie ME métabolisme MI microbiologie MO mortalité NU soins infirmiers PA anatomopathologie PC prévention et contrôle PP physiopathologie PS parasitologie PX psychologie RH rééducation et réadaptation RT radiothérapie SU chirurgie TH thérapie UR urine VE médecine vétérinaire VI virologie |
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DeCS ID: | 52147 | ||||||
Unique ID: | D053529 | ||||||
Documents indexed in the Virtual Health Library (VHL): | Click here to access the VHL documents | ||||||
Date Established: | 2007/01/01 | ||||||
Date of Entry: | 2006/07/05 | ||||||
Revision Date: | 2015/06/22 |
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Naevus spongieux de Cannon
- Preferred
Concept UI |
M0494325 |
Preferred term | Naevus spongieux de Cannon |
Entry term(s) |
Kératose héréditaire des muqueuses Leucokératose héréditaire des muqueuses Maladie de Cannon Naevus blanc spongieux Naevus blanc spongieux de Cannon Naevus blanc spongieux des muqueuses Naevus de Cannon White Sponge Naevus |
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