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Descriptor English: Familial Multiple Lipomatosis
Descriptor Spanish: Lipomatosis Familiar Múltiple
Descriptor lipomatosis familiar múltiple
Entry term(s) adiposis dolorosa tipo III
enfermedad de Dercum tipo III
lipomatosis múltiple hereditaria
Scope note: Trastorno autosómico raro, caracterizado por numerosos lipomas encapsulados en el tronco y las extremidades. Estos lipomas generalmente no son dolorosos, pero pueden causar dolor al crecer. En casos poco frecuentes, un lipoma puede tornarse doloroso y evolucionar a múltiples lipomas dolorosos, lo que se conoce como enfermedad de Dercum de tipo III.
Descriptor Portuguese: Lipomatose Múltipla Familiar
Descriptor French: Lipomatose familiale
Entry term(s): Adipose douloureuse de type 3
Adipose douloureuse de type III
Lipomatose familiale multiple
Lipomatose multiple familiale
Lipome douloureux
Lipomes douloureux
Lipomes multiples familiaux
Maladie de Dercum de type 3
Maladie de Dercum de type III
Tree number(s): C16.320.298
C17.800.463.375
C18.452.584.718.625
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D000071070
Scope note: A rare autosomal disorder characterized by numerous encapsulated lipomas on the trunk and extremities. The lipomas are usually not painful but can cause pain when growing. In rare cases, one lipoma can become painful and progress to multiple painful lipomas; it is then referred to as Dercum's Disease Type III.
Allowable Qualifiers: BL sang
CF liquide cérébrospinal
CI induit chimiquement
CL classification
CO complications
DG imagerie diagnostique
DH diétothérapie
DI diagnostic
DT traitement médicamenteux
EC économie
EH ethnologie
EM embryologie
EN enzymologie
EP épidémiologie
ET étiologie
GE génétique
HI histoire
IM immunologie
ME métabolisme
MI microbiologie
MO mortalité
NU soins infirmiers
PA anatomopathologie
PC prévention et contrôle
PP physiopathologie
PS parasitologie
PX psychologie
RH rééducation et réadaptation
RT radiothérapie
SU chirurgie
TH thérapie
UR urine
VE médecine vétérinaire
VI virologie
DeCS ID: 56401
Unique ID: D000071070
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 2017/01/01
Date of Entry: 2016/07/05
Revision Date: 2016/06/16
Lipomatose familiale - Preferred
Concept UI M000612991
Preferred term Lipomatose familiale
Entry term(s) Lipomatose familiale multiple
Lipomatose multiple familiale
Lipomes multiples familiaux
Maladie de Dercum de type III - Narrower
Concept UI M000612993
Preferred term Maladie de Dercum de type III
Entry term(s) Adipose douloureuse de type 3
Adipose douloureuse de type III
Maladie de Dercum de type 3
Lipome douloureux - Narrower
Concept UI M000612992
Preferred term Lipome douloureux
Entry term(s) Lipomes douloureux



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