Visão selecionada em Inglês
Descritor em português: | Panencefalite Esclerosante Subaguda | ||||||
Descritor em inglês: | Subacute Sclerosing Panencephalitis | ||||||
Descritor em espanhol: |
Panencefalitis Esclerosante Subaguda
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Descritor em francês: | Leucoencéphalite sclérosante subaigüe | ||||||
Termo(s) alternativo(s): |
Encephalitis, Inclusion Body, Measles Inclusion Body Encephalitis, Measles Leukoencephalitides, Subacute Sclerosing Leukoencephalitis, Subacute Sclerosing Leukoencephalitis, Van Bogaert Leukoencephalitis, Van Bogaert's Leukoencephalitis, Van Bogaerts Measles Inclusion Body Encephalitis Panencephalitides, Subacute Sclerosing Panencephalitis, Subacute Sclerosing SSPE Sclerosing Leukoencephalitides, Subacute Sclerosing Leukoencephalitis, Subacute Sclerosing Panencephalitides, Subacute Sclerosing Panencephalitis, Subacute Subacute Sclerosing Leukoencephalitides Subacute Sclerosing Leukoencephalitis Subacute Sclerosing Panencephalitides Van Bogaert Leukoencephalitis Van Bogaert's Leukoencephalitis Van Bogaerts Leukoencephalitis |
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Código(s) hierárquico(s): |
C01.207.245.340.600 C01.207.399.750.600 C01.925.182.525.600 C01.925.782.580.600.500.500.800 C01.925.839.862 C10.228.140.430.520.750.600 C10.228.228.245.340.600 C10.228.228.399.750.600 C10.586.250.520.750.600 |
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Identificador Único RDF: | https://id.nlm.nih.gov/mesh/D013344 | ||||||
Nota de escopo: | A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) |
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Qualificadores permitidos: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy TM transmission UR urine VE veterinary VI virology |
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Indexação Anterior: |
Cerebral Sclerosis, Diffuse (1966-1970) |
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Nota MeSH pública: | 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70 |
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Nota Online: | use SUBACUTE SCLEROSING PANENCEPHALITIS to search VAN BOGAERT'S LEUKOENCEPHALITIS 1971-78; use CEREBRAL SCLEROSIS, DIFFUSE 1966-70 |
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Nota histórica: | 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70 |
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Versão alternativa: | SUBACUTE SCLEROSING PANENCEPH |
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Identificador DeCS: | 13732 | ||||||
ID do descritor: | D013344 | ||||||
Documentos indexados na Biblioteca Virtual em Saúde (BVS): | Clique aqui para acessar os documentos da BVS | ||||||
Data de estabelecimento: | 01/01/1971 | ||||||
Data de entrada: | 01/01/1999 | ||||||
Data de revisão: | 18/06/2019 |
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Subacute Sclerosing Panencephalitis
- Conceito preferido
Identificador do conceito |
M0020645 |
Nota de escopo | A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) |
Termo preferido | Subacute Sclerosing Panencephalitis |
Termo(s) alternativo(s) |
Encephalitis, Inclusion Body, Measles Inclusion Body Encephalitis, Measles Leukoencephalitides, Subacute Sclerosing Leukoencephalitis, Subacute Sclerosing Leukoencephalitis, Van Bogaert Leukoencephalitis, Van Bogaert's Leukoencephalitis, Van Bogaerts Measles Inclusion Body Encephalitis Panencephalitides, Subacute Sclerosing Panencephalitis, Subacute Sclerosing SSPE Sclerosing Leukoencephalitides, Subacute Sclerosing Leukoencephalitis, Subacute Sclerosing Panencephalitides, Subacute Sclerosing Panencephalitis, Subacute Subacute Sclerosing Leukoencephalitides Subacute Sclerosing Leukoencephalitis Subacute Sclerosing Panencephalitides Van Bogaert Leukoencephalitis Van Bogaert's Leukoencephalitis Van Bogaerts Leukoencephalitis |
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