Pesquisa
Descritor em português: Doença Imunoproliferativa do Intestino Delgado
Descritor em inglês: Immunoproliferative Small Intestinal Disease
Descritor em espanhol: Enfermedad Inmunoproliferativa del Intestino Delgado
Descritor enfermedad inmunoproliferativa del intestino delgado
Termo(s) alternativo(s) EIPID
enfermedad de las cadenas alfa
enfermedad de las cadenas pesadas de tipo IgA
linfoma mediterráneo
Nota de escopo: Afección causada por HIPERPLASIA de los LINFOCITOS del INTESTINO DELGADO y los GANGLIOS LINFÁTICOS mesentéricos. Estos linfocitos producen una proteína anómala de cadenas pesadas. Generalmente, los pacientes padecen concomitantemnte un LINFOMA o lo sufren al cabo de unos pocos años. La enfermedad se describió por verz primera en la región mediterránea.
Descritor em francês: Maladie immunoproliférative de l'intestin grêle
Termo(s) alternativo(s): Disease, alpha-Chain
Diseases, alpha-Chain
Heavy Chain Disease, IgA Type
IPSID
Lymphoma, Mediterranean
Mediterranean Lymphoma
alpha Chain Disease
alpha-Chain Disease
alpha-Chain Diseases
Código(s) hierárquico(s): C04.557.386.390
C06.301.371.411.512
C06.405.249.411.512
C06.405.469.491.505
C15.378.147.780.490.512
C15.604.515.435.512
C20.683.515.512
C20.683.780.490.512
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D007161
Nota de escopo: A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Indexação Anterior: Heavy Chain Disease (1966-1986)
Intestinal Neoplasms (1966-1986)
Lymphoma (1966-1986)
Nota MeSH pública: 87
Nota histórica: 87
Versão alternativa: IMMUNOPROLIFERATIVE SMALL INTESTINAL DIS
Identificador DeCS: 19205
ID do descritor: D007161
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1987
Data de entrada: 24/06/1986
Data de revisão: 29/06/2018
Immunoproliferative Small Intestinal Disease - Conceito preferido
Identificador do conceito M0011165
Nota de escopo A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA.
Termo preferido Immunoproliferative Small Intestinal Disease
Termo(s) alternativo(s) Disease, alpha-Chain
Diseases, alpha-Chain
Heavy Chain Disease, IgA Type
IPSID
Lymphoma, Mediterranean
Mediterranean Lymphoma
alpha Chain Disease
alpha-Chain Disease
alpha-Chain Diseases



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