Pesquisa
Descritor em português: Atrofia Muscular Espinal
Descritor em inglês: Muscular Atrophy, Spinal
Descritor em espanhol: Atrofia Muscular Espinal
Descritor atrofia muscular espinal
Termo(s) alternativo(s) atrofia muscular espinal escapuloperonea
atrofia muscular espinal oculofaríngea
atrofia muscular medular oculofaríngea
atrofia muscular medular peroneoescapular
atrofia muscular progresiva
forma escapuloperonea de la atrofia muscular espinal
neuropatía bulboespinal
neuropatía bulbomedular
Nota de escopo: Grupo de trastornos caracterizados por degeneración progresiva de las neuronas motoras de la médula espinal, que genera debilidad y atrofia muscular, generalmente sin datos de lesión de los tractos corticoespinales. Entre las enfermedades de esta categoría se incluyen la enfermedad de Werdnig-Hoffmann y las ATROFIAS MUSCULARES ESPINALES DE LA INFANCIA de comienzo tardío, la mayoría de las cuales son hereditarias. La variante que comienza en la edad adulta se conoce como atrofia muscular progresiva. (Adams et al., Principles of Neurology, 6th ed, p1089)
Descritor em francês: Amyotrophie spinale
Termo(s) alternativo(s): Adult Onset Spinal Muscular Atrophy
Adult Spinal Muscular Atrophy
Adult-Onset Spinal Muscular Atrophy
Amyotrophies, Spinal
Amyotrophy, Neurogenic Scapuloperoneal, New England Type
Amyotrophy, Spinal
Atrophies, Progressive Muscular
Atrophy, Myelopathic Muscular
Atrophy, Progressive Muscular
Atrophy, Spinal Muscular
Bulbospinal Neuronopathies
Bulbospinal Neuronopathy
Distal Spinal Muscular Atrophy
Hereditary Motor Neuronopathies
Hereditary Motor Neuronopathy
Motor Neuronopathies, Hereditary
Motor Neuronopathy, Hereditary
Muscular Atrophies, Progressive
Muscular Atrophy, Adult Spinal
Muscular Atrophy, Myelopathic
Muscular Atrophy, Progressive
Myelopathic Muscular Atrophy
Myelopathic Muscular Atrophy, Progressive
Neuronopathies, Bulbospinal
Neuronopathies, Hereditary Motor
Neuronopathy, Bulbospinal
Neuronopathy, Hereditary Motor
Oculopharyngeal Spinal Muscular Atrophy
Progressive Muscular Atrophies
Progressive Muscular Atrophy
Progressive Myelopathic Muscular Atrophy
Progressive Proximal Myelopathic Muscular Atrophy
Proximal Myelopathic Muscular Atrophy, Progressive
Scapuloperoneal Form of Spinal Muscular Atrophy
Scapuloperoneal Spinal Muscular Atrophy
Spinal Amyotrophies
Spinal Amyotrophy
Spinal Muscular Atrophy
Spinal Muscular Atrophy, Distal
Spinal Muscular Atrophy, Oculopharyngeal
Spinal Muscular Atrophy, Scapuloperoneal
Spinal Muscular Atrophy, Scapuloperoneal Form
Código(s) hierárquico(s): C10.228.854.468
C10.574.562.500
C10.668.467.500
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D009134
Nota de escopo: A group of disorders marked by progressive degeneration of motor neurons in the spinal cord resulting in weakness and muscular atrophy, usually without evidence of injury to the corticospinal tracts. Diseases in this category include Werdnig-Hoffmann disease and later onset SPINAL MUSCULAR ATROPHIES OF CHILDHOOD, most of which are hereditary. (Adams et al., Principles of Neurology, 6th ed, p1089)
Nota de indexação: MUSCULAR ATROPHY, SPINAL, INFANTILE see SPINAL MUSCULAR ATROPHIES OF CHILDHOOD is also available
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Indexação Anterior: Muscular Atrophy (1966-1987)
Spinal Cord Diseases (1966-1987)
Nota MeSH pública: 1988
Nota histórica: 1988
Identificador DeCS: 22949
ID do descritor: D009134
Classificação da NLM: WE 550
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1988
Data de entrada: 10/03/1987
Data de revisão: 23/06/2015
Muscular Atrophy, Spinal - Conceito preferido
Identificador do conceito M0014250
Nota de escopo A group of disorders marked by progressive degeneration of motor neurons in the spinal cord resulting in weakness and muscular atrophy, usually without evidence of injury to the corticospinal tracts. Diseases in this category include Werdnig-Hoffmann disease and later onset SPINAL MUSCULAR ATROPHIES OF CHILDHOOD, most of which are hereditary. (Adams et al., Principles of Neurology, 6th ed, p1089)
Termo preferido Muscular Atrophy, Spinal
Termo(s) alternativo(s) Amyotrophies, Spinal
Amyotrophy, Spinal
Atrophy, Spinal Muscular
Spinal Amyotrophies
Spinal Amyotrophy
Spinal Muscular Atrophy
Distal Spinal Muscular Atrophy - Mais específico
Identificador do conceito M0335740
Termo preferido Distal Spinal Muscular Atrophy
Termo(s) alternativo(s) Spinal Muscular Atrophy, Distal
Hereditary Motor Neuronopathy - Mais específico
Identificador do conceito M0583907
Termo preferido Hereditary Motor Neuronopathy
Termo(s) alternativo(s) Hereditary Motor Neuronopathies
Motor Neuronopathies, Hereditary
Motor Neuronopathy, Hereditary
Neuronopathies, Hereditary Motor
Neuronopathy, Hereditary Motor
Scapuloperoneal Form of Spinal Muscular Atrophy - Mais específico
Identificador do conceito M0335732
Termo preferido Scapuloperoneal Form of Spinal Muscular Atrophy
Termo(s) alternativo(s) Amyotrophy, Neurogenic Scapuloperoneal, New England Type
Scapuloperoneal Spinal Muscular Atrophy
Spinal Muscular Atrophy, Scapuloperoneal
Spinal Muscular Atrophy, Scapuloperoneal Form
Oculopharyngeal Spinal Muscular Atrophy - Mais específico
Identificador do conceito M0335731
Termo preferido Oculopharyngeal Spinal Muscular Atrophy
Termo(s) alternativo(s) Spinal Muscular Atrophy, Oculopharyngeal
Progressive Muscular Atrophy - Mais específico
Identificador do conceito M0393323
Termo preferido Progressive Muscular Atrophy
Termo(s) alternativo(s) Atrophies, Progressive Muscular
Atrophy, Progressive Muscular
Muscular Atrophies, Progressive
Muscular Atrophy, Progressive
Myelopathic Muscular Atrophy, Progressive
Progressive Muscular Atrophies
Progressive Myelopathic Muscular Atrophy
Progressive Proximal Myelopathic Muscular Atrophy - Mais específico
Identificador do conceito M0335741
Termo preferido Progressive Proximal Myelopathic Muscular Atrophy
Termo(s) alternativo(s) Proximal Myelopathic Muscular Atrophy, Progressive
Bulbospinal Neuronopathy - Mais específico
Identificador do conceito M0335730
Termo preferido Bulbospinal Neuronopathy
Termo(s) alternativo(s) Bulbospinal Neuronopathies
Neuronopathies, Bulbospinal
Neuronopathy, Bulbospinal
Myelopathic Muscular Atrophy - Mais específico
Identificador do conceito M0014251
Termo preferido Myelopathic Muscular Atrophy
Termo(s) alternativo(s) Adult Onset Spinal Muscular Atrophy
Adult Spinal Muscular Atrophy
Adult-Onset Spinal Muscular Atrophy
Atrophy, Myelopathic Muscular
Muscular Atrophy, Adult Spinal
Muscular Atrophy, Myelopathic



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