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Descritor em português: | Síndrome de Kartagener | ||||||
Descritor em inglês: | Kartagener Syndrome | ||||||
Descritor em espanhol: |
Síndrome de Kartagener
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Descritor em francês: | Syndrome de Kartagener | ||||||
Termo(s) alternativo(s): |
Bronchiectasis, Polynesian Ciliary Dyskinesia, Primary, 1 Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus Dextrocardia, Bronchiectasis, and Sinusitis Kartagener Triad Kartagener's Syndrome Kartagener's Triad Kartageners Syndrome Kartageners Triad Polynesian Bronchiectases Polynesian Bronchiectasis Siewert Syndrome Syndrome, Kartagener Syndrome, Kartagener's Syndrome, Siewert |
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Código(s) hierárquico(s): |
C08.127.384.500 C08.200.531 C08.695.501 C09.150.531 C14.240.400.280.500 C14.280.400.280.500 C16.131.077.245.500.531 C16.131.240.400.280.500 C16.131.740.501 C16.131.810.250.500 C16.320.184.500.531 C16.320.480 |
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Identificador Único RDF: | https://id.nlm.nih.gov/mesh/D007619 | ||||||
Nota de escopo: | An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts. |
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Qualificadores permitidos: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Nota MeSH pública: | 2002; see KARTAGENER'S SYNDROME 1990-2001; see KARTAGENER TRIAD 1963-1989; for CILIARY DYSKINESIA, PRIMARY see CILIARY MOTILITY DISORDERS 1992-2001 |
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Nota histórica: | 2002 (1963); for CILIARY DYSKINESIA, PRIMARY use CILIARY MOTILITY DISORDERS 1992-2001 |
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Identificador DeCS: | 28293 | ||||||
ID do descritor: | D007619 | ||||||
Documentos indexados na Biblioteca Virtual em Saúde (BVS): | Clique aqui para acessar os documentos da BVS | ||||||
Data de estabelecimento: | 01/01/2002 | ||||||
Data de entrada: | 01/01/1999 | ||||||
Data de revisão: | 01/03/2018 |
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Kartagener Syndrome
- Conceito preferido
Polynesian Bronchiectasis
- Mais específico
Ciliary Dyskinesia, Primary, 1
- Mais específico
Identificador do conceito |
M0011929 |
Nota de escopo | An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts. |
Termo preferido | Kartagener Syndrome |
Termo(s) alternativo(s) |
Dextrocardia, Bronchiectasis, and Sinusitis Kartagener Triad Kartagener's Syndrome Kartagener's Triad Kartageners Syndrome Kartageners Triad Siewert Syndrome Syndrome, Kartagener Syndrome, Kartagener's Syndrome, Siewert |
Identificador do conceito |
M000629770 |
Termo preferido | Polynesian Bronchiectasis |
Termo(s) alternativo(s) |
Bronchiectasis, Polynesian Polynesian Bronchiectases |
Identificador do conceito |
M000629767 |
Termo preferido | Ciliary Dyskinesia, Primary, 1 |
Termo(s) alternativo(s) |
Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus |
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