Pesquisa
Descritor em português: Síndrome de Kartagener
Descritor em inglês: Kartagener Syndrome
Descritor em espanhol: Síndrome de Kartagener
Descritor síndrome de Kartagener
Termo(s) alternativo(s) triada de Kartagener
Nota de escopo: Trastorno autosómico recesivo caracterizado por una tríada de DEXTROCARDIA, INFERTILIDAD y SINUSITIS. El síndrome está causado por mutaciones en los genes de DINEINA que codifican proteínas de movilidad que son componentes de las colas de los espermatozoides y de los CILIOS de los tractos respiratorio y reproductivo.
Descritor em francês: Syndrome de Kartagener
Termo(s) alternativo(s): Bronchiectasis, Polynesian
Ciliary Dyskinesia, Primary, 1
Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus
Dextrocardia, Bronchiectasis, and Sinusitis
Kartagener Triad
Kartagener's Syndrome
Kartagener's Triad
Kartageners Syndrome
Kartageners Triad
Polynesian Bronchiectases
Polynesian Bronchiectasis
Siewert Syndrome
Syndrome, Kartagener
Syndrome, Kartagener's
Syndrome, Siewert
Código(s) hierárquico(s): C08.127.384.500
C08.200.531
C08.695.501
C09.150.531
C14.240.400.280.500
C14.280.400.280.500
C16.131.077.245.500.531
C16.131.240.400.280.500
C16.131.740.501
C16.131.810.250.500
C16.320.184.500.531
C16.320.480
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D007619
Nota de escopo: An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts.
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Nota MeSH pública: 2002; see KARTAGENER'S SYNDROME 1990-2001; see KARTAGENER TRIAD 1963-1989; for CILIARY DYSKINESIA, PRIMARY see CILIARY MOTILITY DISORDERS 1992-2001
Nota histórica: 2002 (1963); for CILIARY DYSKINESIA, PRIMARY use CILIARY MOTILITY DISORDERS 1992-2001
Identificador DeCS: 28293
ID do descritor: D007619
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/2002
Data de entrada: 01/01/1999
Data de revisão: 01/03/2018
Kartagener Syndrome - Conceito preferido
Identificador do conceito M0011929
Nota de escopo An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts.
Termo preferido Kartagener Syndrome
Termo(s) alternativo(s) Dextrocardia, Bronchiectasis, and Sinusitis
Kartagener Triad
Kartagener's Syndrome
Kartagener's Triad
Kartageners Syndrome
Kartageners Triad
Siewert Syndrome
Syndrome, Kartagener
Syndrome, Kartagener's
Syndrome, Siewert
Polynesian Bronchiectasis - Mais específico
Identificador do conceito M000629770
Termo preferido Polynesian Bronchiectasis
Termo(s) alternativo(s) Bronchiectasis, Polynesian
Polynesian Bronchiectases
Ciliary Dyskinesia, Primary, 1 - Mais específico
Identificador do conceito M000629767
Termo preferido Ciliary Dyskinesia, Primary, 1
Termo(s) alternativo(s) Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus



Queremos a sua opinião sobre o novo sitio web do DeCS/MeSH

Convidamos-lhe a responder a uma pesquisa que não levará mais que 3 minutos


Ir para pesquisa