Pesquisa
Descritor em português: Craniofaringioma
Descritor em inglês: Craniopharyngioma
Descritor em espanhol: Craneofaringioma
Descritor craneofaringioma
Termo(s) alternativo(s) craneofaringioma adamantinomatoso
craneofaringioma papilar
tumor de la bolsa de Rathke
Nota de escopo: Neoplasia benigna de la región hipofisaria que se origina a partir de la bolsa de Rathke. Los dos subtipos principales, histológicos y clínicos, son el craneofaringioma adamantino (o clásico) y el craneofaringioma papilar. La forma adamantina se presenta en niños y adolescentes como una formación quística que se expande en la región hipofisaria. La cavidad quística se llena con una sustancia negra y viscosa e histológicamente el tumor está compuesto por epitelio adamantinomatoso y áreas de calcificación y necrosis. Los craneofaringiomas papilares se presentan en adultos, y su característica histológica es la de un epitelio escamoso con papilas. (Joynt, Clinical Neurology, 1998, Ch. 14, p. 50)
Descritor em francês: Craniopharyngiome
Termo(s) alternativo(s): Adamantinous Craniopharyngioma
Adamantinous Craniopharyngiomas
Adult Craniopharyngioma
Adult Craniopharyngiomas
Child Craniopharyngioma
Child Craniopharyngiomas
Craniopharyngioma, Adamantinous
Craniopharyngioma, Adult
Craniopharyngioma, Child
Craniopharyngioma, Papillary
Craniopharyngiomas
Craniopharyngiomas, Adamantinous
Craniopharyngiomas, Adult
Craniopharyngiomas, Child
Craniopharyngiomas, Papillary
Neoplasm, Rathke Cleft
Neoplasm, Rathke's Cleft
Neoplasm, Rathkes Cleft
Papillary Craniopharyngioma
Papillary Craniopharyngiomas
Rathke Cleft Neoplasm
Rathke Pouch Tumor
Rathke's Cleft Neoplasm
Rathke's Pouch Tumor
Rathkes Cleft Neoplasm
Rathkes Pouch Tumor
Tumor, Rathke Pouch
Tumor, Rathke's Pouch
Código(s) hierárquico(s): C04.557.465.625.200
C04.557.580.625.200
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D003397
Nota de escopo: A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma and papillary craniopharyngioma. The adamantinous form presents in children and adolescents as an expanding cystic lesion in the pituitary region. The cystic cavity is filled with a black viscous substance and histologically the tumor is composed of adamantinomatous epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur in adults, and histologically feature a squamous epithelium with papillations. (From Joynt, Clinical Neurology, 1998, Ch14, p50)
Nota de indexação: coord IM with PITUITARY NEOPLASMS (IM)
Qualificadores permitidos: BL blood
BS blood supply
CF cerebrospinal fluid
CH chemistry
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SC secondary
SU surgery
TH therapy
UL ultrastructure
UR urine
VE veterinary
VI virology
Identificador DeCS: 3413
ID do descritor: D003397
Classificação da NLM: WK 585
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1966
Data de entrada: 01/01/1999
Data de revisão: 08/11/1999
Craniopharyngioma - Conceito preferido
Identificador do conceito M0005287
Nota de escopo A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma and papillary craniopharyngioma. The adamantinous form presents in children and adolescents as an expanding cystic lesion in the pituitary region. The cystic cavity is filled with a black viscous substance and histologically the tumor is composed of adamantinomatous epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur in adults, and histologically feature a squamous epithelium with papillations. (From Joynt, Clinical Neurology, 1998, Ch14, p50)
Termo preferido Craniopharyngioma
Termo(s) alternativo(s) Craniopharyngiomas
Neoplasm, Rathke Cleft
Neoplasm, Rathke's Cleft
Neoplasm, Rathkes Cleft
Rathke Cleft Neoplasm
Rathke Pouch Tumor
Rathke's Cleft Neoplasm
Rathke's Pouch Tumor
Rathkes Cleft Neoplasm
Rathkes Pouch Tumor
Tumor, Rathke Pouch
Tumor, Rathke's Pouch
Craniopharyngioma, Papillary - Mais específico
Identificador do conceito M0337314
Termo preferido Craniopharyngioma, Papillary
Termo(s) alternativo(s) Craniopharyngiomas, Papillary
Papillary Craniopharyngioma
Papillary Craniopharyngiomas
Craniopharyngioma, Child - Mais específico
Identificador do conceito M0337316
Termo preferido Craniopharyngioma, Child
Termo(s) alternativo(s) Child Craniopharyngioma
Child Craniopharyngiomas
Craniopharyngiomas, Child
Craniopharyngioma, Adamantinous - Mais específico
Identificador do conceito M0337313
Termo preferido Craniopharyngioma, Adamantinous
Termo(s) alternativo(s) Adamantinous Craniopharyngioma
Adamantinous Craniopharyngiomas
Craniopharyngiomas, Adamantinous
Craniopharyngioma, Adult - Mais específico
Identificador do conceito M0337315
Termo preferido Craniopharyngioma, Adult
Termo(s) alternativo(s) Adult Craniopharyngioma
Adult Craniopharyngiomas
Craniopharyngiomas, Adult



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