Pesquisa
Descritor em português: Dermatomiosite
Descritor em inglês: Dermatomyositis
Descritor em espanhol: Dermatomiositis
Descritor dermatomiositis
Termo(s) alternativo(s) dermatomiositis del adulto
dermatomiositis infantil
dermatopolimiositis
polimiositis-dermatomiositis
Nota de escopo: Enfermedad inflamatoria muscular y cutánea, subaguda o crónica, caracterizada por debilidad de los músculos proximales y erupción cutánea característica. La enfermedad ocurre con una frecuencia aproximadamente igual en niños y adultos. Las lesiones cutáneas generalmente consisten en erupción purpúrica (con menos frecuencia se trata de una dermatitis exfoliativa) que afecta a la nariz, mejillas, frente, parte superior del tronco y brazos. La enfermedad se asocia con una microangiopatía intramuscular mediada por el complemento, que conduce a pérdida de capilares, isquemia muscular, necrosis de fibras musculares, y atrofia perifascicular. La forma infantil de esta enfermedad tiende a evolucionar hacia una vasculitis sistémica. La dermatomiositis puede presentarse en asociación con neoplasias malignas. (Adams et al., Principles of Neurology, 6th ed, pp 1405-6)
Descritor em francês: Dermatomyosite
Termo(s) alternativo(s): Adult Type Dermatomyositis
Childhood Type Dermatomyositis
Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatomyositis, Juvenile
Dermatopolymyositis
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositis
Código(s) hierárquico(s): C05.651.594.819.500
C10.668.491.562.575.500
C17.300.250
C17.800.185
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D003882
Nota de escopo: A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Nota de indexação: coordinate with PARANEOPLASTIC SYNDROMES if pertinent
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Identificador DeCS: 3902
ID do descritor: D003882
Classificação da NLM: WE 550
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1966
Data de entrada: 01/01/1999
Data de revisão: 10/10/2018
Dermatomyositis - Conceito preferido
Identificador do conceito M0006061
Nota de escopo A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Termo preferido Dermatomyositis
Termo(s) alternativo(s) Dermatopolymyositis
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositis
Dermatomyositis, Adult Type - Mais específico
Identificador do conceito M0337306
Termo preferido Dermatomyositis, Adult Type
Termo(s) alternativo(s) Adult Type Dermatomyositis
Dermatomyositis, Childhood Type - Mais específico
Identificador do conceito M0337307
Termo preferido Dermatomyositis, Childhood Type
Termo(s) alternativo(s) Childhood Type Dermatomyositis
Dermatomyositis, Juvenile
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile



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