Visão selecionada em Inglês
Descritor em português: | Papulose Atrófica Maligna | ||||||
Descritor em inglês: | Malignant Atrophic Papulosis | ||||||
Descritor em espanhol: |
Papulosis Atrófica Maligna
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Descritor em francês: | Papulose atrophiante maligne | ||||||
Termo(s) alternativo(s): |
Atrophic Papuloses, Malignant Atrophic Papulosis, Malignant Degos Disease Degos Syndrome Degos's Malignant Atrophic Papulosis Disease, Degos Disease, Kohlmeier-Degos Erythrokeratoderma en cocardes Kohlmeier-Degos Disease Malignant Atrophic Papuloses Papuloses, Malignant Atrophic Papulosis, Malignant Atrophic Syndrome, Degos |
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Código(s) hierárquico(s): |
C14.907.137.520 C14.907.940.530 C17.800.862.457 |
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Identificador Único RDF: | https://id.nlm.nih.gov/mesh/D054853 | ||||||
Nota de escopo: | Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. |
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Nota de indexação: | malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA |
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Qualificadores permitidos: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Nota MeSH pública: | 2008 |
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Nota histórica: | 2008 |
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Identificador DeCS: | 52617 | ||||||
ID do descritor: | D054853 | ||||||
Documentos indexados na Biblioteca Virtual em Saúde (BVS): | Clique aqui para acessar os documentos da BVS | ||||||
Data de estabelecimento: | 01/01/2008 | ||||||
Data de entrada: | 09/07/2007 | ||||||
Data de revisão: | 03/07/2012 |
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Malignant Atrophic Papulosis
- Conceito preferido
Identificador do conceito |
M0508347 |
Nota de escopo | Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. |
Termo preferido | Malignant Atrophic Papulosis |
Termo(s) alternativo(s) |
Atrophic Papuloses, Malignant Atrophic Papulosis, Malignant Degos Disease Degos Syndrome Degos's Malignant Atrophic Papulosis Disease, Degos Disease, Kohlmeier-Degos Erythrokeratoderma en cocardes Kohlmeier-Degos Disease Malignant Atrophic Papuloses Papuloses, Malignant Atrophic Papulosis, Malignant Atrophic Syndrome, Degos |
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