Visão selecionada em Inglês
Descritor em português: | Amiloidose de Cadeia Leve de Imunoglobulina | ||||||
Descritor em inglês: | Immunoglobulin Light-chain Amyloidosis | ||||||
Descritor em espanhol: |
Amiloidosis de Cadenas Ligeras de las Inmunoglobulinas
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Descritor em francês: | Amylose à chaine légère d'immunoglobuline | ||||||
Termo(s) alternativo(s): |
AL Amyloidoses AL Amyloidosis Amyloidoses, Primary Amyloidoses, Primary Systemic Amyloidosis, Immunoglobulin Light chain Amyloidosis, Immunoglobulin Light-chain Amyloidosis, Primary Amyloidosis, Primary Systemic Immunoglobulin Light chain Amyloidosis Immunoglobulin Light-chain Amyloidoses Monoclonal Immunoglobulin Deposition Disease Primary Amyloidoses Primary Amyloidosis Primary Systemic Amyloidoses Primary Systemic Amyloidosis Systemic Amyloidoses, Primary Systemic Amyloidosis, Primary |
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Código(s) hierárquico(s): |
C04.557.595.250 C18.452.845.500.550 C20.683.515.507 C20.683.780.565 |
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Identificador Único RDF: | https://id.nlm.nih.gov/mesh/D000075363 | ||||||
Nota de escopo: | A nonproliferative disorder of the PLASMA CELL characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies. |
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Qualificadores permitidos: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Nota MeSH pública: | 2018; PRIMARY AMYLOIDOSIS was indexed under AMYLOIDOSIS 2010-2017 |
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Nota histórica: | 2018(2010) |
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Identificador DeCS: | 56938 | ||||||
ID do descritor: | D000075363 | ||||||
Documentos indexados na Biblioteca Virtual em Saúde (BVS): | Clique aqui para acessar os documentos da BVS | ||||||
Data de estabelecimento: | 01/01/2018 | ||||||
Data de entrada: | 11/07/2017 | ||||||
Data de revisão: | 20/06/2017 |
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DISEASES
Neoplasms [C04]Neoplasms
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Immunoglobulin Light-chain Amyloidosis
- Conceito preferido
Identificador do conceito |
M000630238 |
Nota de escopo | A nonproliferative disorder of the PLASMA CELL characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies. |
Termo preferido | Immunoglobulin Light-chain Amyloidosis |
Termo(s) alternativo(s) |
AL Amyloidoses AL Amyloidosis Amyloidoses, Primary Amyloidoses, Primary Systemic Amyloidosis, Immunoglobulin Light chain Amyloidosis, Immunoglobulin Light-chain Amyloidosis, Primary Amyloidosis, Primary Systemic Immunoglobulin Light chain Amyloidosis Immunoglobulin Light-chain Amyloidoses Monoclonal Immunoglobulin Deposition Disease Primary Amyloidoses Primary Amyloidosis Primary Systemic Amyloidoses Primary Systemic Amyloidosis Systemic Amyloidoses, Primary Systemic Amyloidosis, Primary |
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