Pesquisa
Descritor em português: Amiloidose de Cadeia Leve de Imunoglobulina
Descritor em inglês: Immunoglobulin Light-chain Amyloidosis
Descritor em espanhol: Amiloidosis de Cadenas Ligeras de las Inmunoglobulinas
Descritor amiloidosis de cadenas ligeras de las inmunoglobulinas
Termo(s) alternativo(s) amiloidosis AL
amiloidosis primaria
amiloidosis primarias
amiloidosis sistémica primaria
amiloidosis sistémicas primarias
enfermedad por depósito de inmunoglobulinas monoclonales
Nota de escopo: Trastorno no proliferativo de las CÉLULAS PLASMÁTICAS caracterizado por una producción excesiva y un plegamiento anómalo de las CADENAS LIGERAS DE LAS INMUNOGLOBULINAS que forman fibrillas amiloideas insolubles (ver DEPÓSITOS AMILOIDES) en diversos tejidos. Entre las manifestaciones clínicas se encuentran el FALLO HEPÁTICO, el MIELOMA MÚLTIPLE, el SÍNDROME NEFRÓTICO, la MIOCARDIOPATÍA RESTRICTIVA y neuropatías.
Descritor em francês: Amylose à chaine légère d'immunoglobuline
Termo(s) alternativo(s): AL Amyloidoses
AL Amyloidosis
Amyloidoses, Primary
Amyloidoses, Primary Systemic
Amyloidosis, Immunoglobulin Light chain
Amyloidosis, Immunoglobulin Light-chain
Amyloidosis, Primary
Amyloidosis, Primary Systemic
Immunoglobulin Light chain Amyloidosis
Immunoglobulin Light-chain Amyloidoses
Monoclonal Immunoglobulin Deposition Disease
Primary Amyloidoses
Primary Amyloidosis
Primary Systemic Amyloidoses
Primary Systemic Amyloidosis
Systemic Amyloidoses, Primary
Systemic Amyloidosis, Primary
Código(s) hierárquico(s): C04.557.595.250
C18.452.845.500.550
C20.683.515.507
C20.683.780.565
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D000075363
Nota de escopo: A nonproliferative disorder of the PLASMA CELL characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Nota MeSH pública: 2018; PRIMARY AMYLOIDOSIS was indexed under AMYLOIDOSIS 2010-2017
Nota histórica: 2018(2010)
Identificador DeCS: 56938
ID do descritor: D000075363
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/2018
Data de entrada: 11/07/2017
Data de revisão: 20/06/2017
Immunoglobulin Light-chain Amyloidosis - Conceito preferido
Identificador do conceito M000630238
Nota de escopo A nonproliferative disorder of the PLASMA CELL characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
Termo preferido Immunoglobulin Light-chain Amyloidosis
Termo(s) alternativo(s) AL Amyloidoses
AL Amyloidosis
Amyloidoses, Primary
Amyloidoses, Primary Systemic
Amyloidosis, Immunoglobulin Light chain
Amyloidosis, Immunoglobulin Light-chain
Amyloidosis, Primary
Amyloidosis, Primary Systemic
Immunoglobulin Light chain Amyloidosis
Immunoglobulin Light-chain Amyloidoses
Monoclonal Immunoglobulin Deposition Disease
Primary Amyloidoses
Primary Amyloidosis
Primary Systemic Amyloidoses
Primary Systemic Amyloidosis
Systemic Amyloidoses, Primary
Systemic Amyloidosis, Primary



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