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Descriptor en español: Succionato-Semialdehído Deshidrogenasa
Descriptor succionato-semialdehído deshidrogenasa
Nota de alcance: Enzima que interviene en el METABOLISMO del GLUTAMATO y del butanoato catalizando la oxidación del succinato-semialdehído a SUCCINATO usando NAD+ como coenzima. La deficiencia de esta enzima causa aciduria 4-hidroxibutírica, un error innato poco frecuente del metabolismo del neurotransmisor ácido 4-aminobutírico (GABA).
Descriptor en inglés: Succinate-Semialdehyde Dehydrogenase
Descriptor en portugués: Succinato-Semialdeído Desidrogenase
Descriptor en francés: Succinate-semialdehyde dehydrogenase
Término(s) alternativo(s): Dehydrogenase, Succinate Semialdehyde
Dehydrogenase, Succinate-Semialdehyde
Dehydrogenase, Succinic Semialdehyde
NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Semialdehyde Dehydrogenase, Succinate
Semialdehyde Dehydrogenase, Succinic
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase
Código(s) jeráquico(s): D08.811.682.657.163.843
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D050644
Nota de alcance: An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).
Calificadores permitidos: AD administration & dosage
AE adverse effects
AI antagonists & inhibitors
AN analysis
BI biosynthesis
BL blood
CF cerebrospinal fluid
CH chemistry
CL classification
CS chemical synthesis
DE drug effects
DF deficiency
EC economics
GE genetics
HI history
IM immunology
IP isolation & purification
ME metabolism
PD pharmacology
PH physiology
PK pharmacokinetics
PO poisoning
RE radiation effects
SD supply & distribution
ST standards
TO toxicity
TU therapeutic use
UL ultrastructure
UR urine
Número de registro: EC 1.2.1.24
Nota Pública de MeSH: 2006; SUCCINATE-SEMIALDEHYDE DEHYDROGENASE was indexed under ALDEHYDE OXIDOREDUCTASES 1977-2005
Nota de historia: 2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979
Identificador de DeCS: 50619
ID del Descriptor: D050644
Documentos indizados en la Biblioteca Virtual de Salud (BVS): Haga clic aquí para acceder a los documentos de la BVS
Fecha de establecimiento: 01/01/2006
Fecha de entrada: 30/06/2005
Succinate-Semialdehyde Dehydrogenase - Concepto preferido
UI del concepto M0079133
Nota de alcance An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).
Término preferido Succinate-Semialdehyde Dehydrogenase
Término(s) alternativo(s) Dehydrogenase, Succinate Semialdehyde
Dehydrogenase, Succinate-Semialdehyde
Dehydrogenase, Succinic Semialdehyde
NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Semialdehyde Dehydrogenase, Succinate
Semialdehyde Dehydrogenase, Succinic
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase



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