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Descriptor English: Arnold-Chiari Malformation
Descriptor Spanish: Malformación de Arnold-Chiari
Descriptor malformación de Arnold-Chiari
Scope note: Grupo de malformaciones congénitas que afectan al tronco encefálico, cerebelo, médula espinal superior, y las estructuras óseas circundantes. El tipo II es el más común, y se caracteriza por compresión de la médula y de las amígdalas cerebelosas que se encuentran dentro del conducto medular cervical superior y MIELOMENINGOCELE asociado. El tipo I tiene características similares, pero con malformaciones menos graves y no tiene mielomeningocele asociado. El tipo III tiene las características del tipo II, con una hernia adicional de todo el cerebelo a través del defecto óseo que afecta al agujero magno, formando un ENCEFALOCELE. El tipo IV es una forma de hipoplasia cerebelosa. Las manifestaciones clínicas de los tipos I-III incluyen TORTÍCOLIS, opistótonos, CEFALEA, VÉRTIGO, PARÁLISIS DE LAS CUERDAS VOCALES, APNEA, NISTAGMO, dificultades de la deglución y ATAXIA. (Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
Descriptor Portuguese: Malformação de Arnold-Chiari
Descriptor French: Malformation d'Arnold-Chiari
Entry term(s): Arnold Chiari Deformity
Arnold Chiari Malformation
Arnold Chiari Malformation, Type 1
Arnold Chiari Malformation, Type 2
Arnold Chiari Malformation, Type 3
Arnold Chiari Malformation, Type 4
Arnold Chiari Malformation, Type I
Arnold Chiari Malformation, Type II
Arnold Chiari Malformation, Type III
Arnold Chiari Malformation, Type IV
Arnold Chiari Syndrome
Arnold-Chiari Deformity
Arnold-Chiari Malformation, Type 1
Arnold-Chiari Malformation, Type 2
Arnold-Chiari Malformation, Type 3
Arnold-Chiari Malformation, Type 4
Arnold-Chiari Malformation, Type I
Arnold-Chiari Malformation, Type II
Arnold-Chiari Malformation, Type III
Arnold-Chiari Malformation, Type IV
Arnold-Chiari Syndrome
Chiari Malformation Type 2
Chiari Malformation Type I
Chiari Malformation Type II
Deformity, Arnold-Chiari
Malformation, Arnold Chiari
Malformation, Arnold-Chiari
Syndrome, Arnold-Chiari
Type I Arnold Chiari Malformation
Type I Arnold-Chiari Malformation
Type II Arnold Chiari Malformation
Type II Arnold-Chiari Malformation
Type III Arnold Chiari Malformation
Type III Arnold-Chiari Malformation
Type IV Arnold Chiari Malformation
Type IV Arnold-Chiari Malformation
Tree number(s): C10.500.680.291
C16.131.666.680.291
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D001139
Scope note: A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
Annotation: do not confuse with CHIARI'S SYNDROME see BUDD-CHIARI SYNDROME
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Public MeSH Note: 2000; see ARNOLD-CHIARI DEFORMITY 1963-1999; for ARNOLD-CHIARI MALFORMATION see ARNOLD-CHIARI DEFORMITY 1963-1999
History Note: 2000(1963)
DeCS ID: 1143
Unique ID: D001139
NLM Classification: WL 101
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1966/01/01
Date of Entry: 1999/01/01
Revision Date: 2014/06/13
Arnold-Chiari Malformation - Preferred
Concept UI M0001704
Scope note A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
Preferred term Arnold-Chiari Malformation
Entry term(s) Arnold Chiari Deformity
Arnold Chiari Malformation
Arnold Chiari Syndrome
Arnold-Chiari Deformity
Arnold-Chiari Syndrome
Deformity, Arnold-Chiari
Malformation, Arnold Chiari
Malformation, Arnold-Chiari
Syndrome, Arnold-Chiari
Arnold-Chiari Malformation, Type II - Narrower
Concept UI M0336997
Preferred term Arnold-Chiari Malformation, Type II
Entry term(s) Arnold Chiari Malformation, Type 2
Arnold Chiari Malformation, Type II
Arnold-Chiari Malformation, Type 2
Chiari Malformation Type 2
Chiari Malformation Type II
Type II Arnold Chiari Malformation
Type II Arnold-Chiari Malformation
Arnold-Chiari Malformation, Type IV - Narrower
Concept UI M0336999
Preferred term Arnold-Chiari Malformation, Type IV
Entry term(s) Arnold Chiari Malformation, Type 4
Arnold Chiari Malformation, Type IV
Arnold-Chiari Malformation, Type 4
Type IV Arnold Chiari Malformation
Type IV Arnold-Chiari Malformation
Arnold-Chiari Malformation, Type I - Narrower
Concept UI M0336996
Preferred term Arnold-Chiari Malformation, Type I
Entry term(s) Arnold Chiari Malformation, Type 1
Arnold Chiari Malformation, Type I
Arnold-Chiari Malformation, Type 1
Chiari Malformation Type I
Type I Arnold Chiari Malformation
Type I Arnold-Chiari Malformation
Arnold-Chiari Malformation, Type III - Narrower
Concept UI M0336998
Preferred term Arnold-Chiari Malformation, Type III
Entry term(s) Arnold Chiari Malformation, Type 3
Arnold Chiari Malformation, Type III
Arnold-Chiari Malformation, Type 3
Type III Arnold Chiari Malformation
Type III Arnold-Chiari Malformation



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