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Descriptor English: Dermatomyositis
Descriptor Spanish: Dermatomiositis
Descriptor dermatomiositis
Entry term(s) dermatomiositis del adulto
dermatomiositis infantil
dermatopolimiositis
polimiositis-dermatomiositis
Scope note: Enfermedad inflamatoria muscular y cutánea, subaguda o crónica, caracterizada por debilidad de los músculos proximales y erupción cutánea característica. La enfermedad ocurre con una frecuencia aproximadamente igual en niños y adultos. Las lesiones cutáneas generalmente consisten en erupción purpúrica (con menos frecuencia se trata de una dermatitis exfoliativa) que afecta a la nariz, mejillas, frente, parte superior del tronco y brazos. La enfermedad se asocia con una microangiopatía intramuscular mediada por el complemento, que conduce a pérdida de capilares, isquemia muscular, necrosis de fibras musculares, y atrofia perifascicular. La forma infantil de esta enfermedad tiende a evolucionar hacia una vasculitis sistémica. La dermatomiositis puede presentarse en asociación con neoplasias malignas. (Adams et al., Principles of Neurology, 6th ed, pp 1405-6)
Descriptor Portuguese: Dermatomiosite
Descriptor French: Dermatomyosite
Entry term(s): Adult Type Dermatomyositis
Childhood Type Dermatomyositis
Dermatomyositis, Adult Type
Dermatomyositis, Childhood Type
Dermatomyositis, Juvenile
Dermatopolymyositis
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositis
Tree number(s): C05.651.594.819.500
C10.668.491.562.575.500
C17.300.250
C17.800.185
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D003882
Scope note: A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Annotation: coordinate with PARANEOPLASTIC SYNDROMES if pertinent
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
DeCS ID: 3902
Unique ID: D003882
NLM Classification: WE 550
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1966/01/01
Date of Entry: 1999/01/01
Revision Date: 2018/10/10
Dermatomyositis - Preferred
Concept UI M0006061
Scope note A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Preferred term Dermatomyositis
Entry term(s) Dermatopolymyositis
Polymyositis Dermatomyositis
Polymyositis-Dermatomyositis
Dermatomyositis, Adult Type - Narrower
Concept UI M0337306
Preferred term Dermatomyositis, Adult Type
Entry term(s) Adult Type Dermatomyositis
Dermatomyositis, Childhood Type - Narrower
Concept UI M0337307
Preferred term Dermatomyositis, Childhood Type
Entry term(s) Childhood Type Dermatomyositis
Dermatomyositis, Juvenile
Juvenile Dermatomyositis
Juvenile Myositis
Myositis, Juvenile



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