DISEASES Cardiovascular Diseases [C14] Cardiovascular Diseases Cardiovascular Abnormalities [C14.240] Cardiovascular Abnormalities Vascular Malformations [C14.240.850] Vascular Malformations Congenital Portosystemic Shunt [C14.240.850.375] Congenital Portosystemic Shunt Arteriovenous Malformations [C14.240.850.750] Arteriovenous Malformations Central Nervous System Vascular Malformations [C14.240.850.875] Central Nervous System Vascular Malformations May-Thurner Syndrome [C14.240.850.906] May-Thurner Syndrome Median Arcuate Ligament Syndrome [C14.240.850.922] Median Arcuate Ligament Syndrome Persistent Left Superior Vena Cava [C14.240.850.930] Persistent Left Superior Vena Cava Pulmonary Atresia [C14.240.850.937] Pulmonary Atresia Scimitar Syndrome [C14.240.850.968] Scimitar Syndrome Single Umbilical Artery [C14.240.850.976] Single Umbilical Artery Vascular Fistula [C14.240.850.984] Vascular Fistula Vascular Ring [C14.240.850.992] Vascular Ring DISEASES Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] Congenital, Hereditary, and Neonatal Diseases and Abnormalities Congenital Abnormalities [C16.131] Congenital Abnormalities Cardiovascular Abnormalities [C16.131.240] Cardiovascular Abnormalities Vascular Malformations [C16.131.240.850] Vascular Malformations Congenital Portosystemic Shunt [C16.131.240.850.250] Congenital Portosystemic Shunt Arterio-Arterial Fistula [C16.131.240.850.500] Arterio-Arterial Fistula Arteriovenous Malformations [C16.131.240.850.750] Arteriovenous Malformations Central Nervous System Vascular Malformations [C16.131.240.850.875] Central Nervous System Vascular Malformations May-Thurner Syndrome [C16.131.240.850.890] May-Thurner Syndrome Median Arcuate Ligament Syndrome [C16.131.240.850.898] Median Arcuate Ligament Syndrome Persistent Left Superior Vena Cava [C16.131.240.850.902] Persistent Left Superior Vena Cava Pulmonary Atresia [C16.131.240.850.906] Pulmonary Atresia Scimitar Syndrome [C16.131.240.850.937] Scimitar Syndrome Single Umbilical Artery [C16.131.240.850.952] Single Umbilical Artery Telangiectasia, Hereditary Hemorrhagic [C16.131.240.850.968] Telangiectasia, Hereditary Hemorrhagic Vascular Ring [C16.131.240.850.984] Vascular Ring

Congenital Portosystemic Shunt - Preferred

Concept UI	M000766784
Scope note	Congenital vascular malformation where the portal venous system blood (PORTAL SYSTEM) bypasses the liver sinusoids and drains into the systemic vein through a shunt.
Preferred term	Congenital Portosystemic Shunt
Entry term(s)	Congenital Portosystemic Shunts Portosystemic Shunt, Congenital Shunt, Congenital Portosystemic

Congenital Intrahepatic Portosystemic Shunt - Narrower

Concept UI	M000766785
Preferred term	Congenital Intrahepatic Portosystemic Shunt

Congenital Extrahepatic Portosystemic Shunt - Narrower

Concept UI	M000766786
Preferred term	Congenital Extrahepatic Portosystemic Shunt
Entry term(s)	Abernethy Malformation Malformation, Abernethy