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Descritor em português: Granulomatose com Poliangiite
Descritor em inglês: Granulomatosis with Polyangiitis
Descritor em espanhol: Granulomatosis con Poliangitis
Descritor granulomatosis con poliangitis
Termo(s) alternativo(s) granulomatosis con poliangeítis
granulomatosis con poliangiítis
granulomatosis de Wegener
Nota de escopo: Enfermedad multisistémica de base genética compleja. Se caracterizada por inflamación de los vasos sanguíneos (VASCULITIS) que conlleva a daños en cualquier número de órganos. Las manifestaciones comunes son inflamación granulomatosa del APARATO RESPIRATORIO y de los riñones. La mayoría de los pacientes tienen autoanticuerpos (ANTICUERPOS ANTICITOPLASMA DE NEUTRÓFILO) frente a MIELOBLASTINA.
Descritor em francês: Granulomatose avec polyangéite
Termo(s) alternativo(s): Granulomatosis with Polyangiitides
Granulomatosis, Wegener
Granulomatosis, Wegener's
Polyangiitides, Granulomatosis with
Polyangiitis, Granulomatosis with
Wegener Granulomatosis
Wegener's Granulomatosis
with Polyangiitides, Granulomatosis
with Polyangiitis, Granulomatosis
Código(s) hierárquico(s): C08.381.483.950
C14.907.940.897.249.750
C17.800.862.105.875
C20.111.193.875
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D014890
Nota de escopo: A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Nota MeSH pública: 2015; see Wegener Granulomatosis 2007-20014
Nota histórica: 2015(1963)
Veja também os descritores: Myeloblastin MeSH
Vasculitis, Central Nervous System MeSH
Identificador DeCS: 27929
ID do descritor: D014890
Classificação da NLM: WF 600
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1966
Data de entrada: 01/01/1999
Data de revisão: 03/07/2012
Granulomatosis with Polyangiitis - Conceito preferido
Identificador do conceito M0022908
Nota de escopo A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.
Termo preferido Granulomatosis with Polyangiitis
Termo(s) alternativo(s) Granulomatosis with Polyangiitides
Granulomatosis, Wegener
Granulomatosis, Wegener's
Polyangiitides, Granulomatosis with
Polyangiitis, Granulomatosis with
Wegener Granulomatosis
Wegener's Granulomatosis
with Polyangiitides, Granulomatosis
with Polyangiitis, Granulomatosis



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