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Descriptor English: Subacute Sclerosing Panencephalitis
Descriptor Spanish: Panencefalitis Esclerosante Subaguda
Descriptor panencefalitis esclerosante subaguda
Entry term(s) PEES
encefalitis por sarampión con cuerpos de inclusión
leucoencefalitis de Van Bogaert
leucoencefalitis esclerosante subaguda
Scope note: Encefalitis rara, lentamente progresiva, causada por la infección crónica por el VIRUS DEL SARAMPIÓN. Afecta principalmente a niños y adultos jóvenes, aproximadamente 2-8 años después de la enfermedad inicial. Tras una pérdida inicial de las habilidades intelectuales y alteraciones de la conducta se producen MIOCLONÍAS progresivas, ESPASTICIDAD MUSCULAR, CONVULSIONES, DEMENCIA, disfunción autónoma y ATAXIA. La MUERTE suele ocurrir 1-3 años después del inicio de la enfermedad. Las características anatomopatológicas incluyen lesiones perivasculares, inclusiones citoplasmáticas eosinofílicas, neurofagia y gliosis fibrosa. La causa el virus SSPE, que es una variante defectuosa del VIRUS DEL SARAMPIÓN. (Adams et al., Principles of Neurology, 6th ed, pp. 767-8)
Descriptor Portuguese: Panencefalite Esclerosante Subaguda
Descriptor French: Leucoencéphalite sclérosante subaigüe
Entry term(s): Encephalitis, Inclusion Body, Measles
Inclusion Body Encephalitis, Measles
Leukoencephalitides, Subacute Sclerosing
Leukoencephalitis, Subacute Sclerosing
Leukoencephalitis, Van Bogaert
Leukoencephalitis, Van Bogaert's
Leukoencephalitis, Van Bogaerts
Measles Inclusion Body Encephalitis
Panencephalitides, Subacute Sclerosing
Panencephalitis, Subacute Sclerosing
SSPE
Sclerosing Leukoencephalitides, Subacute
Sclerosing Leukoencephalitis, Subacute
Sclerosing Panencephalitides, Subacute
Sclerosing Panencephalitis, Subacute
Subacute Sclerosing Leukoencephalitides
Subacute Sclerosing Leukoencephalitis
Subacute Sclerosing Panencephalitides
Van Bogaert Leukoencephalitis
Van Bogaert's Leukoencephalitis
Van Bogaerts Leukoencephalitis
Tree number(s): C01.207.245.340.600
C01.207.399.750.600
C01.925.182.525.600
C01.925.782.580.600.500.500.800
C01.925.839.862
C10.228.140.430.520.750.600
C10.228.228.245.340.600
C10.228.228.399.750.600
C10.586.250.520.750.600
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D013344
Scope note: A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
TM transmission
UR urine
VE veterinary
VI virology
Previous Indexing: Cerebral Sclerosis, Diffuse (1966-1970)
Public MeSH Note: 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
Online Note: use SUBACUTE SCLEROSING PANENCEPHALITIS to search VAN BOGAERT'S LEUKOENCEPHALITIS 1971-78; use CEREBRAL SCLEROSIS, DIFFUSE 1966-70
History Note: 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
Entry Version: SUBACUTE SCLEROSING PANENCEPH
DeCS ID: 13732
Unique ID: D013344
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1971/01/01
Date of Entry: 1999/01/01
Revision Date: 2019/06/18
Subacute Sclerosing Panencephalitis - Preferred
Concept UI M0020645
Scope note A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
Preferred term Subacute Sclerosing Panencephalitis
Entry term(s) Encephalitis, Inclusion Body, Measles
Inclusion Body Encephalitis, Measles
Leukoencephalitides, Subacute Sclerosing
Leukoencephalitis, Subacute Sclerosing
Leukoencephalitis, Van Bogaert
Leukoencephalitis, Van Bogaert's
Leukoencephalitis, Van Bogaerts
Measles Inclusion Body Encephalitis
Panencephalitides, Subacute Sclerosing
Panencephalitis, Subacute Sclerosing
SSPE
Sclerosing Leukoencephalitides, Subacute
Sclerosing Leukoencephalitis, Subacute
Sclerosing Panencephalitides, Subacute
Sclerosing Panencephalitis, Subacute
Subacute Sclerosing Leukoencephalitides
Subacute Sclerosing Leukoencephalitis
Subacute Sclerosing Panencephalitides
Van Bogaert Leukoencephalitis
Van Bogaert's Leukoencephalitis
Van Bogaerts Leukoencephalitis



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