Search
Descriptor English: Neurofibrosarcoma
Descriptor Spanish: Neurofibrosarcoma
Descriptor neurofibrosarcoma
Entry term(s) MPNST
neurilemmosarcomas
neurilemoma maligno
neurilemomas malignos
neurilemosarcoma
neurofibrosarcomas
sarcoma neurogénico
sarcoma neurógeno
sarcomas neurogénicos
schwannoma maligno
schwannomas malignos
schwanoma maligno
schwanomas malignos
tumor maligno de las vainas de los nervios periféricos
tumores malignos de las vainas de los nervios periféricos
Scope note: Tumor maligno que surge de los nervios cutáneos pequeños, es localmente agresivo y puede metastatizar. Histológicamente se caracteriza por células proliferantes atípicas fusiformes con núcleos delgados, ondulados y puntiagudos, zonas hipocelulares y áreas que presentan espirales organizados de proliferación fibroblástica. Los sitios de afectación primaria más frecuentes son las extremidades, el retroperitoneo y el tronco. Estos tumores tienden a presentarse en la infancia, y a menudo se asocian a la NEUROFIBROMATOSIS 1. (DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p. 1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
Descriptor Portuguese: Neurofibrossarcoma
Descriptor French: Neurofibrosarcome
Entry term(s): MPNST
Malignant Neurilemmoma
Malignant Neurilemmomas
Malignant Neurilemoma
Malignant Neurilemomas
Malignant Peripheral Nerve Sheath Tumor
Malignant Peripheral Nerve Sheath Tumors
Malignant Schwannoma
Malignant Schwannomas
Neurilemmoma, Malignant
Neurilemmosarcoma
Neurilemmosarcomas
Neurilemoma, Malignant
Neurofibrosarcomas
Neurogenic Sarcoma
Neurogenic Sarcomas
Peripheral Nerve Sheath Tumors, Malignant
Sarcoma, Neurogenic
Sarcomas, Neurogenic
Schwannoma, Malignant
Tree number(s): C04.557.450.565.590.350.590
C04.557.450.795.350.590
C04.557.580.600.580.795
C10.551.775.500.750.750
C10.668.829.725.500.600.600
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D018319
Scope note: A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
Annotation: coordinate IM with precoordinated organ/neoplasm term (IM)
Allowable Qualifiers: BL blood
BS blood supply
CF cerebrospinal fluid
CH chemistry
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SC secondary
SU surgery
TH therapy
UL ultrastructure
UR urine
VE veterinary
VI virology
Previous Indexing: Fibrosarcoma (1966-1978)
Neurofibroma (1969-1993)
Public MeSH Note: 1994; for Malignant Peripheral Nerve Sheath Tumors, see Neurilemoma 2000-2018
History Note: 1994; for Malignant Peripheral Nerve Sheath Tumors, use Neurilemoma 2000-2018
DeCS ID: 31253
Unique ID: D018319
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1994/01/01
Date of Entry: 1993/06/25
Revision Date: 2018/03/08
Neurofibrosarcoma - Preferred
Concept UI M0027554
Scope note A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)
Preferred term Neurofibrosarcoma
Entry term(s) Neurofibrosarcomas
Neurogenic Sarcoma
Neurogenic Sarcomas
Sarcoma, Neurogenic
Sarcomas, Neurogenic
Malignant Peripheral Nerve Sheath Tumors - Narrower
Concept UI M0336462
Scope note A malignant neurilemmoma with nerve sheath differentiation. It is often associated with NEUROFIBROMATOSIS 1 and RHABDOMYOSARCOMA.
Preferred term Malignant Peripheral Nerve Sheath Tumors
Entry term(s) MPNST
Malignant Neurilemmoma
Malignant Neurilemmomas
Malignant Neurilemoma
Malignant Neurilemomas
Malignant Peripheral Nerve Sheath Tumor
Malignant Schwannoma
Malignant Schwannomas
Neurilemmoma, Malignant
Neurilemmosarcoma
Neurilemmosarcomas
Neurilemoma, Malignant
Peripheral Nerve Sheath Tumors, Malignant
Schwannoma, Malignant



We want your feedback on the new DeCS / MeSH website

We invite you to complete a survey that will take no more than 3 minutes.

Go to survey