DISEASES Hemic and Lymphatic Diseases [C15] Hemic and Lymphatic Diseases Lymphatic Diseases [C15.604] Lymphatic Diseases Histiocytosis [C15.604.250] Histiocytosis Histiocytosis, Non-Langerhans-Cell [C15.604.250.410] Histiocytosis, Non-Langerhans-Cell Erdheim-Chester Disease [C15.604.250.410.224] Erdheim-Chester Disease Histiocytosis, Sinus [C15.604.250.410.450] Histiocytosis, Sinus Lymphohistiocytosis, Hemophagocytic [C15.604.250.410.575] Lymphohistiocytosis, Hemophagocytic Niemann-Pick Diseases [C15.604.250.410.625] Niemann-Pick Diseases Sea-Blue Histiocyte Syndrome [C15.604.250.410.800] Sea-Blue Histiocyte Syndrome Xanthogranuloma, Juvenile [C15.604.250.410.900] Xanthogranuloma, Juvenile

Lymphohistiocytosis, Hemophagocytic - Preferred

Concept UI	M0023960
Scope note	A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.
Preferred term	Lymphohistiocytosis, Hemophagocytic
Entry term(s)	Hemophagocytic Lymphohistiocytoses Hemophagocytic Lymphohistiocytosis Lymphohistiocytoses, Hemophagocytic

Familial Hemophagocytic Lymphocytosis - Narrower

Concept UI	M0480276
Scope note	Rare form of hemophagocytic lymphohistiocytosis with multiorgan involvement seen in infants and young children
Preferred term	Familial Hemophagocytic Lymphocytosis
Entry term(s)	Erythrophagocytic Lymphohistiocytoses, Familial Erythrophagocytic Lymphohistiocytosis, Familial Familial Erythrophagocytic Lymphohistiocytoses Familial Erythrophagocytic Lymphohistiocytosis Familial Hemophagocytic Histiocytoses Familial Hemophagocytic Histiocytosis Familial Hemophagocytic Lymphocytoses Familial Hemophagocytic Lymphohistiocytoses Familial Hemophagocytic Lymphohistiocytosis Familial Hemophagocytic Reticuloses Familial Hemophagocytic Reticulosis Familial Histiocytic Reticuloses Familial Histiocytic Reticulosis Hemophagocytic Histiocytoses, Familial Hemophagocytic Histiocytosis, Familial Hemophagocytic Hymphohistiocytoses, Primary Hemophagocytic Hymphohistiocytosis, Primary Hemophagocytic Lymphocytoses, Familial Hemophagocytic Lymphocytosis, Familial Hemophagocytic Lymphohistiocytoses, Familial Hemophagocytic Lymphohistiocytoses, Primary Hemophagocytic Lymphohistiocytosis, Familial Hemophagocytic Lymphohistiocytosis, Primary Hemophagocytic Reticuloses, Familial Hemophagocytic Reticulosis, Familial Histiocytic Reticuloses, Familial Histiocytic Reticulosis, Familial Histiocytoses, Familial Hemophagocytic Histiocytosis, Familial Hemophagocytic Hymphohistiocytoses, Primary Hemophagocytic Hymphohistiocytosis, Primary Hemophagocytic Lymphocytoses, Familial Hemophagocytic Lymphocytosis, Familial Hemophagocytic Lymphohistiocytoses, Familial Erythrophagocytic Lymphohistiocytoses, Familial Hemophagocytic Lymphohistiocytoses, Primary Hemophagocytic Lymphohistiocytosis, Familial Erythrophagocytic Lymphohistiocytosis, Familial Hemophagocytic Lymphohistiocytosis, Primary Hemophagocytic Primary Hemophagocytic Hymphohistiocytoses Primary Hemophagocytic Hymphohistiocytosis Primary Hemophagocytic Lymphohistiocytoses Primary Hemophagocytic Lymphohistiocytosis Reticuloses, Familial Hemophagocytic Reticuloses, Familial Histiocytic Reticulosis, Familial Hemophagocytic Reticulosis, Familial Histiocytic

Reactive Hemophagocytic Syndrome - Narrower

Concept UI	M0480275
Scope note	Proliferation of HISTIOCYTES in response to viral, bacterial, fungal, or parasitic infections.
Preferred term	Reactive Hemophagocytic Syndrome
Entry term(s)	Hemophagocytic Syndrome, Infection Associated Hemophagocytic Syndrome, Infection-Associated Hemophagocytic Syndrome, Reactive Infection-Associated Hemophagocytic Syndrome

Hemophagocytic Lymphohistiocytosis, Familial, 1 - Narrower

Concept UI	M000647256
Preferred term	Hemophagocytic Lymphohistiocytosis, Familial, 1
Entry term(s)	Hemophagocytic Lymphohistiocytosis Familial -1 Hemophagocytic Lymphohistiocytosis Familial 1

Hemophagocytic Syndromes - Broader

Concept UI	M000648469
Preferred term	Hemophagocytic Syndromes
Entry term(s)	Hemophagocytic Syndrome