Descriptor English: | Erdheim-Chester Disease | ||||||
Descriptor Spanish: |
Enfermedad de Erdheim-Chester
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Descriptor Portuguese: | Doença de Erdheim-Chester | ||||||
Descriptor French: | Maladie d'Erdheim-Chester | ||||||
Entry term(s): |
Erdheim Chester Disease Granulomatosis, Lipid Lipid Granulomatosis |
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Tree number(s): |
C15.604.250.410.224 |
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RDF Unique Identifier: | https://id.nlm.nih.gov/mesh/D031249 | ||||||
Scope note: | A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones. |
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Allowable Qualifiers: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Previous Indexing: |
Histiocytosis (1989-2002) Histiocytosis, Langerhans-Cell (1988-2002) Histiocytosis, Non-Langerhans-Cell (1991-2002) Lipidosis (1979-2002) Xanthomatosis (1979-2002) |
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Public MeSH Note: | 2003 |
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History Note: | 2003 |
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DeCS ID: | 37288 | ||||||
Unique ID: | D031249 | ||||||
Documents indexed in the Virtual Health Library (VHL): | Click here to access the VHL documents | ||||||
Date Established: | 2003/01/01 | ||||||
Date of Entry: | 2002/07/03 | ||||||
Revision Date: | 2008/07/08 |
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Erdheim-Chester Disease
- Preferred
Concept UI |
M0396932 |
Scope note | A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones. |
Preferred term | Erdheim-Chester Disease |
Entry term(s) |
Erdheim Chester Disease Granulomatosis, Lipid Lipid Granulomatosis |
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