Search
Descriptor English: Erdheim-Chester Disease
Descriptor Spanish: Enfermedad de Erdheim-Chester
Descriptor enfermedad de Erdheim-Chester
Entry term(s) granulomatosis lipídica
Scope note: Forma rara de histiocitosis de células no de Langerhans (HISTIOCITOSIS DE CÉLULAS NO DE LANGERHANS) que suele aparecer en la mediana edad. La enfermedad sistémica se caracteriza por infiltración lipídica de los macrófagos, células gigantes multinucleadas, un infiltrado inflamatorio de linfocitos e histiocitos en la médula ósea y esclerosis generalizada de los huesos largos.
Descriptor Portuguese: Doença de Erdheim-Chester
Descriptor French: Maladie d'Erdheim-Chester
Entry term(s): Erdheim Chester Disease
Granulomatosis, Lipid
Lipid Granulomatosis
Tree number(s): C15.604.250.410.224
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D031249
Scope note: A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Previous Indexing: Histiocytosis (1989-2002)
Histiocytosis, Langerhans-Cell (1988-2002)
Histiocytosis, Non-Langerhans-Cell (1991-2002)
Lipidosis (1979-2002)
Xanthomatosis (1979-2002)
Public MeSH Note: 2003
History Note: 2003
DeCS ID: 37288
Unique ID: D031249
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 2003/01/01
Date of Entry: 2002/07/03
Revision Date: 2008/07/08
Erdheim-Chester Disease - Preferred
Concept UI M0396932
Scope note A rare form of non-Langerhans-cell histiocytosis (HISTIOCYTOSIS, NON-LANGERHANS-CELL) with onset in middle age. The systemic disease is characterized by infiltration of lipid-laden macrophages, multinucleated giant cells, an inflammatory infiltrate of lymphocytes and histiocytes in the bone marrow, and a generalized sclerosis of the long bones.
Preferred term Erdheim-Chester Disease
Entry term(s) Erdheim Chester Disease
Granulomatosis, Lipid
Lipid Granulomatosis



We want your feedback on the new DeCS / MeSH website

We invite you to complete a survey that will take no more than 3 minutes.


Go to survey