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Descriptor English: Hemoglobinuria, Paroxysmal
Descriptor Spanish: Hemoglobinuria Paroxística
Descriptor hemoglobinuria paroxística
Entry term(s) hemoglobinuria paroxística a frigore
hemoglobinuria paroxística al frío
hemoglobinuria paroxística nocturna
Scope note: Trastorno que se caracteriza por hemolisis intravascular y hemoglobinuria. Algunos casos se producen como consecuencia de una exposición al frío y son debidas a la presencia de una autohemolisina en el suero. Otros casos se caracterizan por aparecer durante o inmediatamente después del sueño, y se cree que se producen por un defecto intracorpuscular adquirido.
Descriptor Portuguese: Hemoglobinúria Paroxística
Descriptor French: Hémoglobinurie paroxystique
Entry term(s): Cold Paroxysmal Hemoglobinuria
Hemoglobinuria, Cold Paroxysmal
Hemoglobinuria, Nocturnal Paroxysmal
Hemoglobinuria, Paroxysmal Cold
Hemoglobinuria, Paroxysmal Nocturnal
Marchiafava Micheli Syndrome
Marchiafava-Micheli Syndrome
Nocturnal Paroxysmal Hemoglobinuria
Paroxysmal Cold Hemoglobinuria
Paroxysmal Hemoglobinuria
Paroxysmal Hemoglobinuria, Cold
Paroxysmal Hemoglobinuria, Nocturnal
Paroxysmal Nocturnal Hemoglobinuria
Syndrome, Marchiafava-Micheli
Tree number(s): C15.378.071.141.560
C15.378.190.625.460
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D006457
Scope note: A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Public MeSH Note: 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
Online Note: use HEMOGLOBINURIA, PAROXYSMAL to search MARCHIAFAVA-MICHELI SYNDROME 1966-77
History Note: 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
DeCS ID: 6607
Unique ID: D006457
NLM Classification: WJ 344
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1978/01/01
Date of Entry: 1999/01/01
Revision Date: 2013/07/08
Hemoglobinuria, Paroxysmal - Preferred
Concept UI M0010136
Scope note A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
Preferred term Hemoglobinuria, Paroxysmal
Entry term(s) Paroxysmal Hemoglobinuria
Paroxysmal Cold Hemoglobinuria - Narrower
Concept UI M0010138
Preferred term Paroxysmal Cold Hemoglobinuria
Entry term(s) Cold Paroxysmal Hemoglobinuria
Hemoglobinuria, Cold Paroxysmal
Hemoglobinuria, Paroxysmal Cold
Paroxysmal Hemoglobinuria, Cold
Paroxysmal Nocturnal Hemoglobinuria - Narrower
Concept UI M0010137
Preferred term Paroxysmal Nocturnal Hemoglobinuria
Entry term(s) Hemoglobinuria, Nocturnal Paroxysmal
Hemoglobinuria, Paroxysmal Nocturnal
Marchiafava Micheli Syndrome
Marchiafava-Micheli Syndrome
Nocturnal Paroxysmal Hemoglobinuria
Paroxysmal Hemoglobinuria, Nocturnal
Syndrome, Marchiafava-Micheli



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