Descriptor English: | Hemoglobinuria, Paroxysmal | ||||||
Descriptor Spanish: |
Hemoglobinuria Paroxística
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Descriptor Portuguese: | Hemoglobinúria Paroxística | ||||||
Descriptor French: | Hémoglobinurie paroxystique | ||||||
Entry term(s): |
Cold Paroxysmal Hemoglobinuria Hemoglobinuria, Cold Paroxysmal Hemoglobinuria, Nocturnal Paroxysmal Hemoglobinuria, Paroxysmal Cold Hemoglobinuria, Paroxysmal Nocturnal Marchiafava Micheli Syndrome Marchiafava-Micheli Syndrome Nocturnal Paroxysmal Hemoglobinuria Paroxysmal Cold Hemoglobinuria Paroxysmal Hemoglobinuria Paroxysmal Hemoglobinuria, Cold Paroxysmal Hemoglobinuria, Nocturnal Paroxysmal Nocturnal Hemoglobinuria Syndrome, Marchiafava-Micheli |
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Tree number(s): |
C15.378.050.141.560 C15.378.190.625.460 |
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RDF Unique Identifier: | https://id.nlm.nih.gov/mesh/D006457 | ||||||
Scope note: | A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. |
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Allowable Qualifiers: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Public MeSH Note: | 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77 |
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Online Note: | use HEMOGLOBINURIA, PAROXYSMAL to search MARCHIAFAVA-MICHELI SYNDROME 1966-77 |
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History Note: | 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77 |
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DeCS ID: | 6607 | ||||||
Unique ID: | D006457 | ||||||
NLM Classification: | WJ 344 | ||||||
Documents indexed in the Virtual Health Library (VHL): | Click here to access the VHL documents | ||||||
Date Established: | 1978/01/01 | ||||||
Date of Entry: | 1999/01/01 | ||||||
Revision Date: | 2013/07/08 |
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Hemoglobinuria, Paroxysmal
- Preferred
Paroxysmal Cold Hemoglobinuria
- Narrower
Paroxysmal Nocturnal Hemoglobinuria
- Narrower
Concept UI |
M0010136 |
Scope note | A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. |
Preferred term | Hemoglobinuria, Paroxysmal |
Entry term(s) |
Paroxysmal Hemoglobinuria |
Concept UI |
M0010138 |
Preferred term | Paroxysmal Cold Hemoglobinuria |
Entry term(s) |
Cold Paroxysmal Hemoglobinuria Hemoglobinuria, Cold Paroxysmal Hemoglobinuria, Paroxysmal Cold Paroxysmal Hemoglobinuria, Cold |
Concept UI |
M0010137 |
Preferred term | Paroxysmal Nocturnal Hemoglobinuria |
Entry term(s) |
Hemoglobinuria, Nocturnal Paroxysmal Hemoglobinuria, Paroxysmal Nocturnal Marchiafava Micheli Syndrome Marchiafava-Micheli Syndrome Nocturnal Paroxysmal Hemoglobinuria Paroxysmal Hemoglobinuria, Nocturnal Syndrome, Marchiafava-Micheli |
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