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Descriptor English: Bulbar Palsy, Progressive
Descriptor Spanish: Parálisis Bulbar Progresiva
Descriptor parálisis bulbar progresiva
Entry term(s) enfermedad de Fazio-Londe
paresia bulbar progresiva
parálisis bulbar
parálisis bulbar progresiva infantil
síndrome de Fazio-Londe
Scope note: Enfermedad de la neurona motora que se caracteriza por debilidad progresiva de los músculos inervados por los nervios craneales del tronco cerebral inferior. Las manifestaciones clínicas incluyen disartria, disfagia, debilidad facial, debilidad de la lengua y fasciculaciones de la lengua y de los músculos faciales. La forma adulta de la enfermedad se caracteriza inicialmente por debilidad bulbar que progresa hasta afectar a las neuronas motoras a través del neuroeje. A la larga esta afección puede ser indistinguible de la ESCLEROSIS LATERAL AMIOTRÓFICA. El síndrome de Fazio-Londe es una forma hereditaria de esta enfermedad y se presenta en niños y adultos jóvenes. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)
Descriptor Portuguese: Paralisia Bulbar Progressiva
Descriptor French: Paralysie bulbaire progressive
Entry term(s): Bulbar Palsies
Bulbar Palsies, Progressive
Bulbar Palsy
Bulbar Palsy, Progressive, Of Childhood
Bulbar Paralyses
Bulbar Paralysis
Childhood Progressive Bulbar Palsy
Fazio-Londe Disease
Fazio-Londe Syndrome
Fazio-Londe's Disease
Fazio-Londe's Syndrome
Palsies, Bulbar
Palsies, Progressive Bulbar
Palsy, Bulbar
Palsy, Progressive Bulbar
Paralysis, Bulbar
Progressive Bulbar Palsies
Progressive Bulbar Palsy
Progressive Bulbar Palsy of Childhood
Tree number(s): C10.574.562.300
C10.668.467.300
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D010244
Scope note: A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Public MeSH Note: 2000; see PARALYSIS, BULBAR 1966-1999
History Note: 2000(1966)
DeCS ID: 10433
Unique ID: D010244
NLM Classification: WL 310
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 2000/01/01
Date of Entry: 1999/01/01
Revision Date: 2016/06/08
Bulbar Palsy, Progressive - Preferred
Concept UI M0015879
Scope note A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)
Preferred term Bulbar Palsy, Progressive
Entry term(s) Bulbar Palsies, Progressive
Palsies, Progressive Bulbar
Palsy, Progressive Bulbar
Progressive Bulbar Palsies
Progressive Bulbar Palsy
Bulbar Palsy - Broader
Concept UI M000618614
Preferred term Bulbar Palsy
Entry term(s) Bulbar Palsies
Bulbar Paralyses
Bulbar Paralysis
Palsies, Bulbar
Palsy, Bulbar
Paralysis, Bulbar
Childhood Progressive Bulbar Palsy - Narrower
Concept UI M0337043
Preferred term Childhood Progressive Bulbar Palsy
Entry term(s) Bulbar Palsy, Progressive, Of Childhood
Fazio-Londe Disease
Fazio-Londe Syndrome
Fazio-Londe's Disease
Fazio-Londe's Syndrome
Progressive Bulbar Palsy of Childhood



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