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Descriptor English: Aspartylglucosylaminase
Descriptor Spanish: Aspartilglucosilaminasa
Descriptor aspartilglucosilaminasa
Entry term(s) aspartilglicosamina amidohidrolasa
aspartilglucosaminidasa
aspartilglucosilamina desaspartilasa
glicosilasparaginasa
Scope note: Enzima que cataliza la conversión de N(4)-(beta-N-acetil-D-glucosaminil)-L-asparragina y agua en N-acetil-beta-D-glucosaminilamina y L-aspartato. Actúa sólo sobre oligosacáridos de asparragina que contienen un aminoácido, es decir, la ASPARRAGINA tiene grupos libres alfa-amino y alfa-carboxilo. (Enzyme Nomenclature, 1992)
Descriptor Portuguese: Aspartilglucosilaminase
Descriptor French: N4-(beta-N-acetylglucosaminyl)-L-asparaginase
Entry term(s): Aspartylglucosylaminase
Aspartylglucosylamine deaspartylase
Tree number(s): D08.811.277.087.125
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D001227
Scope note: An enzyme that catalyzes the conversion of N(4)-(beta-N-acetyl-D-glucosaminyl)-L-asparagine and water to N-acetyl-beta-D-glucosaminylamine and L-aspartate. It acts only on asparagine-oligosaccharides containing one amino acid, i.e. the ASPARAGINE has free alpha-amino and alpha-carboxyl groups. (From Enzyme Nomenclature, 1992)
Allowable Qualifiers: AD administration et posologie
AE effets indésirables
AI antagonistes et inhibiteurs
AN analyse
BI biosynthèse
BL sang
CF liquide cérébrospinal
CH composition chimique
CL classification
CS synthèse chimique
DE effets des médicaments et des substances chimiques
EC économie
GE génétique
HI histoire
IM immunologie
IP isolement et purification
ME métabolisme
PD pharmacologie
PH physiologie
PK pharmacocinétique
PO intoxication
RE effets des radiations
SD ressources et distribution
ST normes
TO toxicité
TU usage thérapeutique
UL ultrastructure
UR urine
Entry Combination: deficiency:Aspartylglucosaminuria
Registry Number: EC 3.5.1.26
CAS Type 1 Name: N(4)-(beta-N-Acetyl-D-glucosaminyl)-L-asparagine amidohydrolase
DeCS ID: 1234
Unique ID: D001227
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1991/01/01
Date of Entry: 1974/11/19
Revision Date: 2008/07/08
N4-(beta-N-acetylglucosaminyl)-L-asparaginase - Preferred
Concept UI M0001849
Preferred term N4-(beta-N-acetylglucosaminyl)-L-asparaginase
Entry term(s) Aspartylglucosylaminase
Aspartylglucosylamine deaspartylase



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