| Descriptor English: | Hereditary Sensory and Autonomic Neuropathies | ||||||
| Descriptor Spanish: |
Neuropatías Hereditarias Sensoriales y Autónomas
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| Descriptor Portuguese: | Neuropatias Hereditárias Sensoriais e Autônomas | ||||||
| Descriptor French: | Neuropathies héréditaires sensitives et autonomes | ||||||
| Entry term(s): |
Acroosteolyses, Neurogenic Acroosteolysis, Giaccai Type Acroosteolysis, Neurogenic Congenital Insensitivity to Pain with Anhidrosis Congenital Sensory Neuropathies Congenital Sensory Neuropathy Familial Dysautonomia, Type 2 Familial Dysautonomia, Type II Giaccai Type Acroosteolysis HSAN HSAN (Hereditary Sensory Autonomic Neuropathy) HSAN 1 HSAN 4 HSAN 5 HSAN I HSAN IV HSAN Type I HSAN Type II HSAN Type IV HSAN Type V HSAN V HSAN2 HSAN5 HSANII HSANs (Hereditary Sensory Autonomic Neuropathy) HSN Type I HSN Type II HSN Type IIs Hereditary Sensory And Autonomic Neuropathy IV Hereditary Sensory Autonomic Neuropathy, Type 1 Hereditary Sensory Autonomic Neuropathy, Type 2 Hereditary Sensory Autonomic Neuropathy, Type 4 Hereditary Sensory Autonomic Neuropathy, Type 5 Hereditary Sensory Neuropathies Hereditary Sensory Neuropathy Hereditary Sensory Neuropathy Type 1 Hereditary Sensory Neuropathy Type I Hereditary Sensory Neuropathy Type Ia Hereditary Sensory Radicular Neuropathy Hereditary Sensory Radicular Neuropathy, Recessive Form Hereditary Sensory and Autonomic Neuropathy 4 Hereditary Sensory and Autonomic Neuropathy Type 1 Hereditary Sensory and Autonomic Neuropathy Type 2 Hereditary Sensory and Autonomic Neuropathy Type I Hereditary Sensory and Autonomic Neuropathy Type II Hereditary Sensory and Autonomic Neuropathy Type IV Hereditary Sensory and Autonomic Neuropathy Type V Hereditary Sensory and Autonomic Neuropathy, Type 4 Hereditary Sensory and Autonomic Neuropathy, Type 5 Insensitivity to Pain with Anhidrosis, Congenital Insensitivity to Pain, Congenital, with Anhidrosis Neurogenic Acroosteolyses Neurogenic Acroosteolysis Neuropathies, Congenital Sensory Neuropathies, Hereditary Sensory Neuropathies, Hereditary Sensory and Autonomic Neuropathy Hereditary Sensory Radicular, Autosomal Dominant Neuropathy Hereditary Sensory and Autonomic Type 1 Neuropathy, Congenital Sensory Neuropathy, Congenital Sensory, with Anhidrosis Neuropathy, Hereditary Sensory Neuropathy, Hereditary Sensory And Autonomic, Type I Neuropathy, Hereditary Sensory And Autonomic, Type V Neuropathy, Hereditary Sensory Radicular, Autosomal Dominant Neuropathy, Hereditary Sensory Radicular, Autosomal Recessive Neuropathy, Hereditary Sensory, Type I Neuropathy, Progressive Sensory, Of Children Pain Insensitivity with Anhidrosis, Congenital Sensory Neuropathies, Congenital Sensory Neuropathies, Hereditary Sensory Neuropathy, Congenital Sensory Neuropathy, Hereditary Sensory and Autonomic Neuropathies, Hereditary Type I, HSAN Type I, HSN Type IV, HSAN |
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| Tree number(s): |
C10.500.250 C10.574.500.493 C10.668.829.800.175 C16.131.666.310 C16.320.400.415 |
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| RDF Unique Identifier: | https://id.nlm.nih.gov/mesh/D009477 | ||||||
| Scope note: | A group of inherited disorders characterized by degeneration of dorsal root and autonomic ganglion cells, and clinically by loss of sensation and autonomic dysfunction. There are five subtypes. Type I features autosomal dominant inheritance and distal sensory involvement. Type II is characterized by autosomal inheritance and distal and proximal sensory loss. Type III is DYSAUTONOMIA, FAMILIAL. Type IV features insensitivity to pain, heat intolerance, and mental deficiency. Type V is characterized by a selective loss of pain with intact light touch and vibratory sensation. (From Joynt, Clinical Neurology, 1995, Ch51, pp142-4) |
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| Annotation: | do not confuse with HEREDITARY SENSORY AND MOTOR NEUROPATHY; note entry terms for HSAN types: HSAN TYPE III see DYSAUTONOMIA, FAMILIAL is also available |
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| Allowable Qualifiers: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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| Previous Indexing: |
Peripheral Nerve Diseases (1966-1978) Peripheral Nerves (1966-1978) Sensation (1966-1978) |
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| Public MeSH Note: | 2000; see NEUROPATHIES, HEREDITARY SENSORY AND AUTONOMIC 1989-1999; see NEUROPATHY, HEREDITARY SENSORY 1979-1988 |
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| History Note: | 2000(1989); use NEUROPATHY, HEREDITARY SENSORY 1979-1988 |
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| Entry Version: | HEREDITARY SENSORY AUTONOMIC NEUROPATHIES |
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| Related: |
Pain Insensitivity, Congenital
MeSH | ||||||
| DeCS ID: | 23938 | ||||||
| Unique ID: | D009477 | ||||||
| Documents indexed in the Virtual Health Library (VHL): | Click here to access the VHL documents | ||||||
| Date Established: | 1979/01/01 | ||||||
| Date of Entry: | 1999/11/08 | ||||||
| Revision Date: | 2018/06/30 |
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Hereditary Sensory and Autonomic Neuropathies
- Preferred
Hereditary Sensory and Autonomic Neuropathy Type V
- Narrower
Hereditary Sensory Neuropathy Type I
- Narrower
HSAN Type IV
- Narrower
Sensory Neuropathy, Hereditary
- Narrower
Hereditary Sensory and Autonomic Neuropathy Type II
- Narrower
Hereditary Sensory Radicular Neuropathy
- Narrower
| Concept UI |
M0014743 |
| Scope note | A group of inherited disorders characterized by degeneration of dorsal root and autonomic ganglion cells, and clinically by loss of sensation and autonomic dysfunction. There are five subtypes. Type I features autosomal dominant inheritance and distal sensory involvement. Type II is characterized by autosomal inheritance and distal and proximal sensory loss. Type III is DYSAUTONOMIA, FAMILIAL. Type IV features insensitivity to pain, heat intolerance, and mental deficiency. Type V is characterized by a selective loss of pain with intact light touch and vibratory sensation. (From Joynt, Clinical Neurology, 1995, Ch51, pp142-4) |
| Preferred term | Hereditary Sensory and Autonomic Neuropathies |
| Entry term(s) |
HSAN HSAN (Hereditary Sensory Autonomic Neuropathy) HSANs (Hereditary Sensory Autonomic Neuropathy) Neuropathies, Hereditary Sensory and Autonomic Sensory and Autonomic Neuropathies, Hereditary |
| Concept UI |
M0583610 |
| Preferred term | Hereditary Sensory and Autonomic Neuropathy Type V |
| Entry term(s) |
HSAN 5 HSAN Type V HSAN V HSAN5 Hereditary Sensory Autonomic Neuropathy, Type 5 Hereditary Sensory and Autonomic Neuropathy, Type 5 Neuropathy, Hereditary Sensory And Autonomic, Type V |
| Concept UI |
M0583611 |
| Preferred term | Hereditary Sensory Neuropathy Type I |
| Entry term(s) |
HSAN 1 HSAN I HSAN Type I HSN Type I Hereditary Sensory Autonomic Neuropathy, Type 1 Hereditary Sensory Neuropathy Type 1 Hereditary Sensory Neuropathy Type Ia Hereditary Sensory and Autonomic Neuropathy Type 1 Hereditary Sensory and Autonomic Neuropathy Type I Neuropathy Hereditary Sensory Radicular, Autosomal Dominant Neuropathy Hereditary Sensory and Autonomic Type 1 Neuropathy, Hereditary Sensory And Autonomic, Type I Neuropathy, Hereditary Sensory Radicular, Autosomal Dominant Neuropathy, Hereditary Sensory, Type I Type I, HSAN Type I, HSN |
| Concept UI |
M0014741 |
| Preferred term | HSAN Type IV |
| Entry term(s) |
Congenital Insensitivity to Pain with Anhidrosis Familial Dysautonomia, Type 2 Familial Dysautonomia, Type II HSAN 4 HSAN IV Hereditary Sensory And Autonomic Neuropathy IV Hereditary Sensory Autonomic Neuropathy, Type 4 Hereditary Sensory and Autonomic Neuropathy 4 Hereditary Sensory and Autonomic Neuropathy Type IV Hereditary Sensory and Autonomic Neuropathy, Type 4 Insensitivity to Pain with Anhidrosis, Congenital Insensitivity to Pain, Congenital, with Anhidrosis Neuropathy, Congenital Sensory, with Anhidrosis Pain Insensitivity with Anhidrosis, Congenital Type IV, HSAN |
| Concept UI |
M0014745 |
| Preferred term | Sensory Neuropathy, Hereditary |
| Entry term(s) |
Acroosteolyses, Neurogenic Acroosteolysis, Neurogenic Congenital Sensory Neuropathies Congenital Sensory Neuropathy Hereditary Sensory Neuropathies Hereditary Sensory Neuropathy Neurogenic Acroosteolyses Neurogenic Acroosteolysis Neuropathies, Congenital Sensory Neuropathies, Hereditary Sensory Neuropathy, Congenital Sensory Neuropathy, Hereditary Sensory Sensory Neuropathies, Congenital Sensory Neuropathies, Hereditary Sensory Neuropathy, Congenital |
| Concept UI |
M0583609 |
| Preferred term | Hereditary Sensory and Autonomic Neuropathy Type II |
| Entry term(s) |
Acroosteolysis, Giaccai Type Giaccai Type Acroosteolysis HSAN Type II HSAN2 HSANII HSN Type II HSN Type IIs Hereditary Sensory Autonomic Neuropathy, Type 2 Hereditary Sensory Radicular Neuropathy, Recessive Form Hereditary Sensory and Autonomic Neuropathy Type 2 Neuropathy, Hereditary Sensory Radicular, Autosomal Recessive Neuropathy, Progressive Sensory, Of Children |
| Concept UI |
M0014744 |
| Preferred term | Hereditary Sensory Radicular Neuropathy |
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