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Descriptor in English: Dandy-Walker Syndrome
Descriptor in Spanish: Síndrome de Dandy-Walker
Descriptor in Portuguese: Síndrome de Dandy-Walker
Descriptor in French: Syndrome de Dandy-Walker
Entry term(s): Cyst, Dandy-Walker
Cysts, Dandy-Walker
Dandy Walker Complex
Dandy Walker Deformity
Dandy Walker Malformation
Dandy Walker Syndrome
Dandy Walker Syndrome, Familial
Dandy-Walker Complex
Dandy-Walker Complices
Dandy-Walker Cyst
Dandy-Walker Cysts
Dandy-Walker Deformities
Dandy-Walker Deformity
Dandy-Walker Malformation
Dandy-Walker Syndrome, Familial
Familial Dandy-Walker Syndrome
Hydrocephalus, Internal, Dandy-Walker Type
Hydrocephalus, Noncommunicating, Dandy-Walker Type
Luschka Magendie Foramina Atresia
Luschka-Magendie Foramina Atresia
Malformation, Dandy-Walker
Tree number(s): C10.228.140.252.300
C10.228.140.602.500
C10.500.205
C16.131.666.205
Scope note: A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
History Note: 1991(1970)
DeCS UI: 3635
Descriptor UI: D003616
Date Established: 1991/01/01
Date of Entry: 1999/01/01
Revision Date: 2016/01/20
Dandy-Walker Syndrome - Preferred
Concept UI M0005653
Scope note A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)
Preferred term Dandy-Walker Syndrome
Entry term(s) Cyst, Dandy-Walker
Cysts, Dandy-Walker
Dandy Walker Complex
Dandy Walker Deformity
Dandy Walker Malformation
Dandy Walker Syndrome
Dandy-Walker Complex
Dandy-Walker Complices
Dandy-Walker Cyst
Dandy-Walker Cysts
Dandy-Walker Deformities
Dandy-Walker Deformity
Dandy-Walker Malformation
Hydrocephalus, Internal, Dandy-Walker Type
Hydrocephalus, Noncommunicating, Dandy-Walker Type
Luschka Magendie Foramina Atresia
Luschka-Magendie Foramina Atresia
Malformation, Dandy-Walker
Dandy-Walker Syndrome, Familial - Narrower
Concept UI M000610906
Preferred term Dandy-Walker Syndrome, Familial
Entry term(s) Dandy Walker Syndrome, Familial
Familial Dandy-Walker Syndrome



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