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Descriptor en español: |
Dermatomiositis
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Descriptor en inglés: | Dermatomyositis | ||||||
Descriptor en portugués: | Dermatomiosite | ||||||
Descriptor en francés: | Dermatomyosite | ||||||
Término(s) alternativo(s): |
Adult Type Dermatomyositis Childhood Type Dermatomyositis Dermatomyositis, Adult Type Dermatomyositis, Childhood Type Dermatomyositis, Juvenile Dermatopolymyositis Juvenile Dermatomyositis Juvenile Myositis Myositis, Juvenile Polymyositis Dermatomyositis Polymyositis-Dermatomyositis |
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Código(s) jeráquico(s): |
C05.651.594.819.500 C10.668.491.562.575.500 C17.300.250 C17.800.185 |
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Identificador Único RDF: | https://id.nlm.nih.gov/mesh/D003882 | ||||||
Nota de alcance: | A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) |
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Nota de indización: | coordinate with PARANEOPLASTIC SYNDROMES if pertinent |
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Calificadores permitidos: |
BL blood CF cerebrospinal fluid CI chemically induced CL classification CN congenital CO complications DG diagnostic imaging DH diet therapy DI diagnosis DT drug therapy EC economics EH ethnology EM embryology EN enzymology EP epidemiology ET etiology GE genetics HI history IM immunology ME metabolism MI microbiology MO mortality NU nursing PA pathology PC prevention & control PP physiopathology PS parasitology PX psychology RH rehabilitation RT radiotherapy SU surgery TH therapy UR urine VE veterinary VI virology |
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Identificador de DeCS: | 3902 | ||||||
ID del Descriptor: | D003882 | ||||||
Clasificación de la NLM: | WE 550 | ||||||
Documentos indizados en la Biblioteca Virtual de Salud (BVS): | Haga clic aquí para acceder a los documentos de la BVS | ||||||
Fecha de establecimiento: | 01/01/1966 | ||||||
Fecha de entrada: | 01/01/1999 | ||||||
Fecha de revisión: | 10/10/2018 |
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Dermatomyositis
- Concepto preferido
Dermatomyositis, Adult Type
- Más estrecho
Dermatomyositis, Childhood Type
- Más estrecho
UI del concepto |
M0006061 |
Nota de alcance | A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) |
Término preferido | Dermatomyositis |
Término(s) alternativo(s) |
Dermatopolymyositis Polymyositis Dermatomyositis Polymyositis-Dermatomyositis |
UI del concepto |
M0337306 |
Término preferido | Dermatomyositis, Adult Type |
Término(s) alternativo(s) |
Adult Type Dermatomyositis |
UI del concepto |
M0337307 |
Término preferido | Dermatomyositis, Childhood Type |
Término(s) alternativo(s) |
Childhood Type Dermatomyositis Dermatomyositis, Juvenile Juvenile Dermatomyositis Juvenile Myositis Myositis, Juvenile |
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