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Descriptor English: Ichthyosiform Erythroderma, Congenital
Descriptor Spanish: Eritrodermia Ictiosiforme Congénita
Descriptor eritrodermia ictiosiforme congénita
Scope note: Este término se utiliza para designar algunas formas graves de ictiosis observadas en el recien naciod, que se caracteriza por escamas hiperquerotósicas. Los neonatos pueden encontrarse envueltos en una membrana coloide que puede comenzar a desprenderse en las primeras 24 horas. A lo largo de las dos semanas siguientes se produce un proceso de descamación persistente. De esta enfermedad exisiten formas bullosas (HIPERQUERATOSIS EPIDERMOLÍTICA), no bullosas, (ICTIOSIS LAMELAR), de tipo húmedo y seco.
Descriptor Portuguese: Eritrodermia Ictiosiforme Congênita
Descriptor French: Érythrodermie ichtyosiforme congénitale
Entry term(s): Congenital Ichthyosiform Erythroderma
Congenital Ichthyosiform Erythroderma, Dry Type
Congenital Ichthyosiform Erythroderma, Wet Type
Congenital Ichthyosiform Erythrodermas
Erythroderma, Congenital Ichthyosiform
Erythrodermas, Congenital Ichthyosiform
Ichthyosiform Erythrodermas, Congenital
Tree number(s): C16.131.831.512.400
C16.320.850.400
C16.614.492.400
C17.800.428.333.250
C17.800.804.512.400
C17.800.827.400
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D016113
Scope note: Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
Annotation: an ichthyosis rather than an erythroderma; do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Previous Indexing: Ichthyosis (1966-1990)
Public MeSH Note: 91
History Note: 91
Entry Version: ICHTHYOSIFORM ERYTHRODERMA CONGEN
DeCS ID: 28985
Unique ID: D016113
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1991/01/01
Date of Entry: 1990/02/12
Revision Date: 2015/06/18
Ichthyosiform Erythroderma, Congenital - Preferred
Concept UI M0024612
Scope note Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
Preferred term Ichthyosiform Erythroderma, Congenital
Entry term(s) Congenital Ichthyosiform Erythroderma
Congenital Ichthyosiform Erythrodermas
Erythroderma, Congenital Ichthyosiform
Erythrodermas, Congenital Ichthyosiform
Ichthyosiform Erythrodermas, Congenital
Congenital Ichthyosiform Erythroderma, Wet Type - Narrower
Concept UI M0024614
Preferred term Congenital Ichthyosiform Erythroderma, Wet Type
Congenital Ichthyosiform Erythroderma, Dry Type - Narrower
Concept UI M0024613
Preferred term Congenital Ichthyosiform Erythroderma, Dry Type



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