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Descriptor English: Incontinentia Pigmenti
Descriptor Spanish: Incontinencia Pigmentaria
Descriptor Portuguese: Incontinência Pigmentar
Descriptor French: Incontinentia pigmenti
Entry term(s): Bloch Sulzberger Syndrome
Bloch-Siemens Syndrome
Bloch-Siemens-Sulzberger Syndrome
Bloch-Sulzberger Syndrome
Syndrome, Bloch-Sulzberger
Tree number(s): C16.131.077.445
C16.131.831.580
C16.320.850.420
C17.800.621.497
C17.800.804.580
C17.800.827.420
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D007184
Scope note: A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Annotation: multiple skin & other abnorm; do not confuse with INCONTINENTIA PIGMENTI ACHROMIANS see PIGMENTATION DISORDERS
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Previous Indexing: Pigmentation Disorders (1966-1986)
Public MeSH Note: 91; was see under PIGMENTATION DISORDERS 1987-90
History Note: 91(87); was see under PIGMENTATION DISORDERS 1987-90
DeCS ID: 19206
Unique ID: D007184
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 1991/01/01
Date of Entry: 1986/04/03
Revision Date: 2016/07/01
Incontinentia Pigmenti - Preferred
Concept UI M0011200
Scope note A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Preferred term Incontinentia Pigmenti
Entry term(s) Bloch Sulzberger Syndrome
Bloch-Siemens Syndrome
Bloch-Siemens-Sulzberger Syndrome
Bloch-Sulzberger Syndrome
Syndrome, Bloch-Sulzberger



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