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Descriptor English: Malignant Atrophic Papulosis
Descriptor Spanish: Papulosis Atrófica Maligna
Descriptor papulosis atrófica maligna
Entry term(s) enfermedad de Degos
enfermedad de Degos-Kohlmeier
Scope note: Descrita de formas diversas, como vasculopatía, endovasculitis o arteriopatía obliterante, esta afección presenta una forma benigna cutánea y una variante generalizada, multiorgánica, letal. Se caracteriza por estrechamiento y obstrucción de la luz de los vasos sanguíneos de tamaño pequeño a mediano, que da lugar a isquemia e infarto de los órganos y sistemas afectados. Se desconocen la etiología y fisiopatología.
Descriptor Portuguese: Papulose Atrófica Maligna
Descriptor French: Papulose atrophiante maligne
Entry term(s): Atrophic Papuloses, Malignant
Atrophic Papulosis, Malignant
Degos Disease
Degos Syndrome
Degos's Malignant Atrophic Papulosis
Disease, Degos
Disease, Kohlmeier-Degos
Erythrokeratoderma en cocardes
Kohlmeier-Degos Disease
Malignant Atrophic Papuloses
Papuloses, Malignant Atrophic
Papulosis, Malignant Atrophic
Syndrome, Degos
Tree number(s): C14.907.137.520
C14.907.940.530
C17.800.862.457
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D054853
Scope note: Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
Annotation: malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA
Allowable Qualifiers: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CN congenital
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Public MeSH Note: 2008
History Note: 2008
DeCS ID: 52617
Unique ID: D054853
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 2008/01/01
Date of Entry: 2007/07/09
Revision Date: 2012/07/03
Malignant Atrophic Papulosis - Preferred
Concept UI M0508347
Scope note Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
Preferred term Malignant Atrophic Papulosis
Entry term(s) Atrophic Papuloses, Malignant
Atrophic Papulosis, Malignant
Degos Disease
Degos Syndrome
Degos's Malignant Atrophic Papulosis
Disease, Degos
Disease, Kohlmeier-Degos
Erythrokeratoderma en cocardes
Kohlmeier-Degos Disease
Malignant Atrophic Papuloses
Papuloses, Malignant Atrophic
Papulosis, Malignant Atrophic
Syndrome, Degos



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