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Descriptor English: Isovaleryl-CoA Dehydrogenase
Descriptor Spanish: Isovaleril-CoA Deshidrogenasa
Descriptor isovaleril-CoA deshidrogenasa
Scope note: Flavoproteína mitocondrial que cataliza la oxidación del 3-metilbutanoil-CoA a 3-metilbut-2-enoil-CoA usando FAD como cofactor. Los defectos de esta enzima se asocian a acidemia isovalérica (AIV).
Descriptor Portuguese: Isovaleril-CoA Desidrogenase
Descriptor French: Isovaleryl-CoA dehydrogenase
Entry term(s): CoA Dehydrogenase, Isovaleryl
Dehydrogenase, Isovaleryl CoA
Dehydrogenase, Isovaleryl-CoA
Dehydrogenase, Isovaleryl-Coenzyme A
Isovaleryl CoA Dehydrogenase
Isovaleryl Coenzyme A Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase
Tree number(s): D08.811.682.660.462
RDF Unique Identifier: https://id.nlm.nih.gov/mesh/D050769
Scope note: A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Allowable Qualifiers: AD administration & dosage
AE adverse effects
AI antagonists & inhibitors
AN analysis
BI biosynthesis
BL blood
CF cerebrospinal fluid
CH chemistry
CL classification
CS chemical synthesis
DE drug effects
DF deficiency
EC economics
GE genetics
HI history
IM immunology
IP isolation & purification
ME metabolism
PD pharmacology
PH physiology
PK pharmacokinetics
PO poisoning
RE radiation effects
SD supply & distribution
ST standards
TO toxicity
TU therapeutic use
UL ultrastructure
UR urine
Registry Number: EC 1.3.8.4
Previous Indexing: Acyl Coenzyme A (1980-1982)
Coenzyme A (1973-1980)
Oxidoreductases (1983-2003)
Oxidoreductases Acting on CH-CH Group Donors (2004-2005)
Valerates (1973-1982)
Public MeSH Note: 2006; ISOVALERYL-COA DEHYDROGENASE was indexed under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005, under OXIDOREDUCTASES 1983-2003, under ACYL COENZYME A 1980-1982, COENZYME A 1973-1980, and under VALERATES 1973-1982
History Note: 2006(1973)
DeCS ID: 50628
Unique ID: D050769
Documents indexed in the Virtual Health Library (VHL): Click here to access the VHL documents
Date Established: 2006/01/01
Date of Entry: 2005/06/30
Revision Date: 2016/06/28
Isovaleryl-CoA Dehydrogenase - Preferred
Concept UI M0076387
Scope note A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
Preferred term Isovaleryl-CoA Dehydrogenase
Entry term(s) CoA Dehydrogenase, Isovaleryl
Dehydrogenase, Isovaleryl CoA
Dehydrogenase, Isovaleryl-CoA
Dehydrogenase, Isovaleryl-Coenzyme A
Isovaleryl CoA Dehydrogenase
Isovaleryl Coenzyme A Dehydrogenase
Isovaleryl-Coenzyme A Dehydrogenase



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