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Descritor em português: Poroceratose
Descritor em inglês: Porokeratosis
Descritor em espanhol: Poroqueratosis
Descritor poroqueratosis
Termo(s) alternativo(s) poroqueratosis actínica superficial diseminada
poroqueratosis de Mibelli
poroqueratosis lineal
poroqueratosis palmar y plantar diseminada
poroqueratosis palmoplantar
poroqueratosis punctata
Nota de escopo: Raro trastorno crónico, autosómico dominante, que se ve con mayor frecuencia en hombres y que usualmente aparece temprano en la niñez. Se caracteriza por la formación de parches ligeramente atróficos rodeados por un borde queratótico elevado.
Descritor em francês: Porokératose
Termo(s) alternativo(s): Disseminated Superficial Actinic Porokeratosis
Keratoderma Palmoplantar, Punctate Type 2
Linear Porokeratosis
Mibelli Porokeratosis
Palmoplantar Porokeratosis
Porokeratosis Palmaris et Plantaris Disseminata
Porokeratosis Plantaris Palmaris et Disseminata
Porokeratosis Plantaris, Palmaris, Et Disseminata
Porokeratosis of Mibelli
Porokeratosis, Disseminated Superficial Actinic
Porokeratosis, Disseminated Superficial Actinic 2
Porokeratosis, Disseminated Superficial Actinic, 2
Porokeratosis, Linear
Porokeratosis, Mibelli
Porokeratosis, Palmar, Plantar, And Disseminated 1
Porokeratosis, Palmoplantar
Porokeratosis, Punctate
Punctate Porokeratosis
Type 2 Punctate PPK
Código(s) hierárquico(s): C16.320.850.730
C17.800.428.750
C17.800.827.730
Identificador Único RDF: https://id.nlm.nih.gov/mesh/D017499
Nota de escopo: A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.
Nota de indexação: do not confuse with PARAKERATOSIS
Qualificadores permitidos: BL blood
CF cerebrospinal fluid
CI chemically induced
CL classification
CO complications
DG diagnostic imaging
DH diet therapy
DI diagnosis
DT drug therapy
EC economics
EH ethnology
EM embryology
EN enzymology
EP epidemiology
ET etiology
GE genetics
HI history
IM immunology
ME metabolism
MI microbiology
MO mortality
NU nursing
PA pathology
PC prevention & control
PP physiopathology
PS parasitology
PX psychology
RH rehabilitation
RT radiotherapy
SU surgery
TH therapy
UR urine
VE veterinary
VI virology
Indexação Anterior: Keratosis (1966-1992)
Nota MeSH pública: 93
Nota histórica: 93
Identificador DeCS: 30610
ID do descritor: D017499
Documentos indexados na Biblioteca Virtual em Saúde (BVS): Clique aqui para acessar os documentos da BVS
Data de estabelecimento: 01/01/1993
Data de entrada: 22/05/1992
Data de revisão: 22/06/2015
Porokeratosis - Conceito preferido
Identificador do conceito M0026551
Nota de escopo A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.
Termo preferido Porokeratosis
Porokeratosis, Disseminated Superficial Actinic - Mais específico
Identificador do conceito M0376740
Termo preferido Porokeratosis, Disseminated Superficial Actinic
Termo(s) alternativo(s) Disseminated Superficial Actinic Porokeratosis
Porokeratosis, Palmoplantar - Mais específico
Identificador do conceito M0026550
Termo preferido Porokeratosis, Palmoplantar
Termo(s) alternativo(s) Keratoderma Palmoplantar, Punctate Type 2
Palmoplantar Porokeratosis
Porokeratosis Palmaris et Plantaris Disseminata
Porokeratosis Plantaris Palmaris et Disseminata
Porokeratosis Plantaris, Palmaris, Et Disseminata
Porokeratosis, Palmar, Plantar, And Disseminated 1
Type 2 Punctate PPK
Porokeratosis, Linear - Mais específico
Identificador do conceito M0376741
Termo preferido Porokeratosis, Linear
Termo(s) alternativo(s) Linear Porokeratosis
Porokeratosis, Mibelli - Mais específico
Identificador do conceito M0376739
Nota de escopo The classical form of porokeratosis with isolated lesions.
Termo preferido Porokeratosis, Mibelli
Termo(s) alternativo(s) Mibelli Porokeratosis
Porokeratosis of Mibelli
Porokeratosis, Punctate - Mais específico
Identificador do conceito M0376742
Termo preferido Porokeratosis, Punctate
Termo(s) alternativo(s) Punctate Porokeratosis
Porokeratosis, Disseminated Superficial Actinic 2 - Relacionado, mas não mais amplo ou mais específico
Identificador do conceito M0530801
Termo preferido Porokeratosis, Disseminated Superficial Actinic 2
Termo(s) alternativo(s) Porokeratosis, Disseminated Superficial Actinic, 2



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