DISEASES Nervous System Diseases [C10] Nervous System Diseases Neuromuscular Diseases [C10.668] Neuromuscular Diseases Peripheral Nervous System Diseases [C10.668.829] Peripheral Nervous System Diseases Polyneuropathies [C10.668.829.800] Polyneuropathies Alcoholic Neuropathy [C10.668.829.800.050] Alcoholic Neuropathy Hereditary Sensory and Autonomic Neuropathies [C10.668.829.800.175] Hereditary Sensory and Autonomic Neuropathies Hereditary Sensory and Motor Neuropathy [C10.668.829.800.300] Hereditary Sensory and Motor Neuropathy Paraneoplastic Polyneuropathy [C10.668.829.800.662] Paraneoplastic Polyneuropathy POEMS Syndrome [C10.668.829.800.700] POEMS Syndrome Polyradiculoneuropathy [C10.668.829.800.750] Polyradiculoneuropathy Tangier Disease [C10.668.829.800.875] Tangier Disease DISEASES Hemic and Lymphatic Diseases [C15] Hemic and Lymphatic Diseases Hematologic Diseases [C15.378] Hematologic Diseases Blood Protein Disorders [C15.378.147] Blood Protein Disorders Paraproteinemias [C15.378.147.780] Paraproteinemias Cryoglobulinemia [C15.378.147.780.243] Cryoglobulinemia Heavy Chain Disease [C15.378.147.780.490] Heavy Chain Disease Monoclonal Gammopathy of Undetermined Significance [C15.378.147.780.570] Monoclonal Gammopathy of Undetermined Significance Multiple Myeloma [C15.378.147.780.650] Multiple Myeloma POEMS Syndrome [C15.378.147.780.750] POEMS Syndrome Smoldering Multiple Myeloma [C15.378.147.780.838] Smoldering Multiple Myeloma Waldenstrom Macroglobulinemia [C15.378.147.780.925] Waldenstrom Macroglobulinemia DISEASES Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16] Congenital, Hereditary, and Neonatal Diseases and Abnormalities Congenital Abnormalities [C16.131] Congenital Abnormalities Abnormalities, Multiple [C16.131.077] Abnormalities, Multiple 22q11 Deletion Syndrome [C16.131.077.019] 22q11 Deletion Syndrome Alagille Syndrome [C16.131.077.065] Alagille Syndrome Angelman Syndrome [C16.131.077.095] Angelman Syndrome Barth Syndrome [C16.131.077.121] Barth Syndrome Basal Cell Nevus Syndrome [C16.131.077.130] Basal Cell Nevus Syndrome Beckwith-Wiedemann Syndrome [C16.131.077.133] Beckwith-Wiedemann Syndrome Bloom Syndrome [C16.131.077.137] Bloom Syndrome Branchio-Oto-Renal Syndrome [C16.131.077.208] Branchio-Oto-Renal Syndrome Carney Complex [C16.131.077.229] Carney Complex Ciliopathies [C16.131.077.245] Ciliopathies Cockayne Syndrome [C16.131.077.250] Cockayne Syndrome Costello Syndrome [C16.131.077.256] Costello Syndrome Cri-du-Chat Syndrome [C16.131.077.262] Cri-du-Chat Syndrome De Lange Syndrome [C16.131.077.272] De Lange Syndrome Deaf-Blind Disorders [C16.131.077.299] Deaf-Blind Disorders Donohue Syndrome [C16.131.077.313] Donohue Syndrome Down Syndrome [C16.131.077.327] Down Syndrome Ectodermal Dysplasia [C16.131.077.350] Ectodermal Dysplasia Fraser Syndrome [C16.131.077.371] Fraser Syndrome Gardner Syndrome [C16.131.077.393] Gardner Syndrome Heterotaxy Syndrome [C16.131.077.401] Heterotaxy Syndrome Holoprosencephaly [C16.131.077.410] Holoprosencephaly Incontinentia Pigmenti [C16.131.077.445] Incontinentia Pigmenti Isolated Noncompaction of the Ventricular Myocardium [C16.131.077.477] Isolated Noncompaction of the Ventricular Myocardium Laurence-Moon Syndrome [C16.131.077.509] Laurence-Moon Syndrome LEOPARD Syndrome [C16.131.077.525] LEOPARD Syndrome Loeys-Dietz Syndrome [C16.131.077.537] Loeys-Dietz Syndrome Marfan Syndrome [C16.131.077.550] Marfan Syndrome Mobius Syndrome [C16.131.077.578] Mobius Syndrome Monilethrix [C16.131.077.592] Monilethrix Nail-Patella Syndrome [C16.131.077.606] Nail-Patella Syndrome Netherton Syndrome [C16.131.077.619] Netherton Syndrome Nevus, Sebaceous of Jadassohn [C16.131.077.633] Nevus, Sebaceous of Jadassohn Oculocerebrorenal Syndrome [C16.131.077.662] Oculocerebrorenal Syndrome Orofaciodigital Syndromes [C16.131.077.676] Orofaciodigital Syndromes Pallister-Hall Syndrome [C16.131.077.690] Pallister-Hall Syndrome Pentalogy of Cantrell [C16.131.077.696] Pentalogy of Cantrell POEMS Syndrome [C16.131.077.703] POEMS Syndrome Polycystic Kidney Diseases [C16.131.077.717] Polycystic Kidney Diseases Prader-Willi Syndrome [C16.131.077.730] Prader-Willi Syndrome Prolidase Deficiency [C16.131.077.735] Prolidase Deficiency Proteus Syndrome [C16.131.077.740] Proteus Syndrome Prune Belly Syndrome [C16.131.077.745] Prune Belly Syndrome Rubella Syndrome, Congenital [C16.131.077.790] Rubella Syndrome, Congenital Rubinstein-Taybi Syndrome [C16.131.077.804] Rubinstein-Taybi Syndrome Short Rib-Polydactyly Syndrome [C16.131.077.850] Short Rib-Polydactyly Syndrome Silver-Russell Syndrome [C16.131.077.855] Silver-Russell Syndrome Smith-Lemli-Opitz Syndrome [C16.131.077.860] Smith-Lemli-Opitz Syndrome Smith-Magenis Syndrome [C16.131.077.879] Smith-Magenis Syndrome Sotos Syndrome [C16.131.077.889] Sotos Syndrome Trichothiodystrophy Syndromes [C16.131.077.899] Trichothiodystrophy Syndromes Trisomy 13 Syndrome [C16.131.077.919] Trisomy 13 Syndrome Trisomy 18 Syndrome [C16.131.077.929] Trisomy 18 Syndrome Waardenburg Syndrome [C16.131.077.938] Waardenburg Syndrome Weill-Marchesani Syndrome [C16.131.077.941] Weill-Marchesani Syndrome Wolf-Hirschhorn Syndrome [C16.131.077.944] Wolf-Hirschhorn Syndrome Zellweger Syndrome [C16.131.077.970] Zellweger Syndrome DISEASES Immune System Diseases [C20] Immune System Diseases Immunoproliferative Disorders [C20.683] Immunoproliferative Disorders Paraproteinemias [C20.683.780] Paraproteinemias Cryoglobulinemia [C20.683.780.250] Cryoglobulinemia Heavy Chain Disease [C20.683.780.490] Heavy Chain Disease Immunoglobulin Light-chain Amyloidosis [C20.683.780.565] Immunoglobulin Light-chain Amyloidosis Monoclonal Gammopathy of Undetermined Significance [C20.683.780.640] Monoclonal Gammopathy of Undetermined Significance Multiple Myeloma [C20.683.780.650] Multiple Myeloma POEMS Syndrome [C20.683.780.750] POEMS Syndrome Smoldering Multiple Myeloma [C20.683.780.838] Smoldering Multiple Myeloma Waldenstrom Macroglobulinemia [C20.683.780.925] Waldenstrom Macroglobulinemia

POEMS Syndrome - Conceito preferido

Identificador do conceito	M0025682
Nota de escopo	A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62)
Termo preferido	POEMS Syndrome
Termo(s) alternativo(s)	Crow Fukase Syndrome Crow-Fukase Syndrome Organomegalies, Polyneuropathy Organomegaly, Polyneuropathy Polyneuropathy Organomegalies Polyneuropathy Organomegaly Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome Syndrome, Crow-Fukase Syndrome, POEMS Syndrome, Takatsuki's Takatsuki Syndrome Takatsuki's Syndrome